Synonyms,Symbol,Description
P08574,CYC1,cytochrome c-1
P21912,SDHB,"succinate dehydrogenase complex, subunit B, iron sulfur (Ip)"
Q99807,COQ7,"coenzyme Q7 homolog, ubiquinone (yeast)"
P31040,SDHA,"succinate dehydrogenase complex, subunit A, flavoprotein (Fp)"
P31930,UQCRC1,ubiquinol-cytochrome c reductase core protein I
Q5HYK3,COQ5,"coenzyme Q5 homolog, methyltransferase (S. cerevisiae)"
P08559,PDHA1,pyruvate dehydrogenase (lipoamide) alpha 1
O75208,COQ9,coenzyme Q9
P52815,MRPL12,mitochondrial ribosomal protein L12
P30049,ATP5D,"ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit"
P20674,COX5A,cytochrome c oxidase subunit Va
Q86U28,ISCA2,iron-sulfur cluster assembly 2
O75439,PMPCB,peptidase (mitochondrial processing) beta
P47985,UQCRFS1,"ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1"
P25705,ATP5A1,"ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle"
Q02218,OGDH,oxoglutarate (alpha-ketoglutarate) dehydrogenase (lipoamide)
P11177,PDHB,pyruvate dehydrogenase (lipoamide) beta
P22695,UQCRC2,ubiquinol-cytochrome c reductase core protein II
O14521,SDHD,"succinate dehydrogenase complex, subunit D, integral membrane protein"
P82673,MRPS35,mitochondrial ribosomal protein S35
O14949,UQCRQ,"ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa"
Q96EL3,MRPL53,mitochondrial ribosomal protein L53
P11182,DBT,dihydrolipoamide branched chain transacylase E2
Q16654,PDK4,"pyruvate dehydrogenase kinase, isozyme 4"
P40926,MDH2,"malate dehydrogenase 2, NAD (mitochondrial)"
Q92552,MRPS27,mitochondrial ribosomal protein S27
O75390,CS,citrate synthase
Q9HAV7,GRPEL1,"GrpE-like 1, mitochondrial (E. coli)"
P10515,DLAT,dihydrolipoamide S-acetyltransferase
P42704,LRPPRC,leucine-rich pentatricopeptide repeat containing
P36957,DLST,dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex)
O00330,PDHX,"pyruvate dehydrogenase complex, component X"
Q96RP9,GFM1,"G elongation factor, mitochondrial 1"
O95563,MPC2,mitochondrial pyruvate carrier 2
P28331,NDUFS1,"NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase)"
Q9H2W6,MRPL46,mitochondrial ribosomal protein L46
P56381,ATP5E,"ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit"
Q00325,SLC25A3,"solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3"
Q9Y3D9,MRPS23,mitochondrial ribosomal protein S23
P07954,FH,fumarate hydratase
Q10713,PMPCA,peptidase (mitochondrial processing) alpha
P06576,ATP5B,"ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide"
Q5VUM1,C6orf57,chromosome 6 open reading frame 57
Q9UDW1,UQCR10,"ubiquinol-cytochrome c reductase, complex III subunit X"
Q9BUE6,ISCA1,iron-sulfur cluster assembly 1
Q9P2R7,SUCLA2,"succinate-CoA ligase, ADP-forming, beta subunit"
Q9NZJ6,COQ3,coenzyme Q3 methyltransferase
Q9NSE4,IARS2,"isoleucyl-tRNA synthetase 2, mitochondrial"
P82914,MRPS15,mitochondrial ribosomal protein S15
P50213,IDH3A,isocitrate dehydrogenase 3 (NAD+) alpha
Q9Y6N1,COX11,cytochrome c oxidase assembly homolog 11 (yeast)
Q16134,ETFDH,electron-transferring-flavoprotein dehydrogenase
P62072,TIMM10,translocase of inner mitochondrial membrane 10 homolog (yeast)
Q9BQ48,MRPL34,mitochondrial ribosomal protein L34
Q5T653,MRPL2,mitochondrial ribosomal protein L2
P12694,BCKDHA,"branched chain keto acid dehydrogenase E1, alpha polypeptide"
P07919,UQCRH,ubiquinol-cytochrome c reductase hinge protein
Q9BW72,HIGD2A,"HIG1 hypoxia inducible domain family, member 2A"
P48047,ATP5O,"ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit"
P30084,ECHS1,"enoyl CoA hydratase, short chain, 1, mitochondrial"
Q6P1Q0,LETMD1,LETM1 domain containing 1
P12074,COX6A1,cytochrome c oxidase subunit VIa polypeptide 1
Q7KZN9,COX15,cytochrome c oxidase assembly homolog 15 (yeast)
Q9Y4W6,AFG3L2,AFG3-like AAA ATPase 2
P40939,HADHA,"hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit"
P13804,ETFA,"electron-transfer-flavoprotein, alpha polypeptide"
O75251,NDUFS7,"NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase)"
P23786,CPT2,carnitine palmitoyltransferase 2
P21953,BCKDHB,"branched chain keto acid dehydrogenase E1, beta polypeptide"
O43837,IDH3B,isocitrate dehydrogenase 3 (NAD+) beta
Q15031,LARS2,"leucyl-tRNA synthetase 2, mitochondrial"
P16219,ACADS,"acyl-CoA dehydrogenase, C-2 to C-3 short chain"
O95202,LETM1,leucine zipper-EF-hand containing transmembrane protein 1
P56385,ATP5I,"ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E"
O60313,OPA1,optic atrophy 1 (autosomal dominant)
Q13825,AUH,AU RNA binding protein/enoyl-CoA hydratase
P53597,SUCLG1,"succinate-CoA ligase, alpha subunit"
P19404,NDUFV2,"NADH dehydrogenase (ubiquinone) flavoprotein 2, 24kDa"
Q9Y2Z9,COQ6,coenzyme Q6 monooxygenase
Q8N983,MRPL43,mitochondrial ribosomal protein L43
Q8NFV4,ABHD11,abhydrolase domain containing 11
P18859,ATP5J,"ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6"
O95169,NDUFB8,"NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa"
P36776,LONP1,"lon peptidase 1, mitochondrial"
P09622,DLD,dihydrolipoamide dehydrogenase
O95831,AIFM1,"apoptosis-inducing factor, mitochondrion-associated, 1"
Q96DC8,ECHDC3,enoyl CoA hydratase domain containing 3
Q6UXV4,APOOL,apolipoprotein O-like
Q7Z7H8,MRPL10,mitochondrial ribosomal protein L10
Q96E11,MRRF,mitochondrial ribosome recycling factor
O00217,NDUFS8,"NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase)"
P11310,ACADM,"acyl-CoA dehydrogenase, C-4 to C-12 straight chain"
Q16891,IMMT,"inner membrane protein, mitochondrial"
Q9Y5J7,TIMM9,translocase of inner mitochondrial membrane 9 homolog (yeast)
P12235,SLC25A4,"solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4"
Q9Y512,SAMM50,SAMM50 sorting and assembly machinery component
O75306,NDUFS2,"NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase)"
P49821,NDUFV1,"NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa"
Q99798,ACO2,"aconitase 2, mitochondrial"
Q8IYB8,SUPV3L1,"suppressor of var1, 3-like 1 (S. cerevisiae)"
P22830,FECH,ferrochelatase
P46199,MTIF2,mitochondrial translational initiation factor 2
P35232,PHB,prohibitin
Q6NVY1,HIBCH,3-hydroxyisobutyryl-CoA hydrolase
Q9Y399,MRPS2,mitochondrial ribosomal protein S2
P38646,HSPA9,heat shock 70kDa protein 9 (mortalin)
Q15526,SURF1,surfeit 1
P30048,PRDX3,peroxiredoxin 3
Q9H3K2,GHITM,growth hormone inducible transmembrane protein
Q8N442,GUF1,GUF1 GTPase homolog (S. cerevisiae)
Q9Y5L4,TIMM13,translocase of inner mitochondrial membrane 13 homolog (yeast)
Q9HD34,LYRM4,LYR motif containing 4
Q9NX20,MRPL16,mitochondrial ribosomal protein L16
Q9NQ50,MRPL40,mitochondrial ribosomal protein L40
P51553,IDH3G,isocitrate dehydrogenase 3 (NAD+) gamma
Q99643,SDHC,"succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa"
O43674,NDUFB5,"NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa"
Q9NX18,SDHAF2,succinate dehydrogenase complex assembly factor 2
Q96MF6,COQ10A,coenzyme Q10 homolog A (S. cerevisiae)
P30042,C21orf33,chromosome 21 open reading frame 33
Q99757,TXN2,thioredoxin 2
Q9NVS2,MRPS18A,mitochondrial ribosomal protein S18A
P09669,COX6C,cytochrome c oxidase subunit VIc
Q9Y6M9,NDUFB9,"NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa"
Q9Y6C9,MTCH2,mitochondrial carrier 2
P56556,NDUFA6,"NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa"
O43772,SLC25A20,"solute carrier family 25 (carnitine/acylcarnitine translocase), member 20"
Q9BYD6,MRPL1,mitochondrial ribosomal protein L1
O43615,TIMM44,translocase of inner mitochondrial membrane 44 homolog (yeast)
Q14061,COX17,COX17 cytochrome c oxidase copper chaperone
Q5TGZ0,MINOS1,mitochondrial inner membrane organizing system 1
P04179,SOD2,"superoxide dismutase 2, mitochondrial"
P14854,COX6B1,cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous)
P21796,VDAC1,voltage-dependent anion channel 1
Q16740,CLPP,caseinolytic mitochondrial matrix peptidase proteolytic subunit
Q16836,HADH,hydroxyacyl-CoA dehydrogenase
P28330,ACADL,"acyl-CoA dehydrogenase, long chain"
P24752,ACAT1,acetyl-CoA acetyltransferase 1
Q96EH3,MALSU1,mitochondrial assembly of ribosomal large subunit 1
O76031,CLPX,caseinolytic mitochondrial matrix peptidase chaperone subunit
O43181,NDUFS4,"NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase)"
Q9BYD3,MRPL4,mitochondrial ribosomal protein L4
Q07021,C1QBP,"complement component 1, q subcomponent binding protein"
Q5JRX3,PITRM1,pitrilysin metallopeptidase 1
Q9NVA1,UQCC1,ubiquinol-cytochrome c reductase complex assembly factor 1
Q7Z7F7,MRPL55,mitochondrial ribosomal protein L55
Q6IN84,MRM1,mitochondrial rRNA methyltransferase 1 homolog (S. cerevisiae)
Q9BV79,MECR,mitochondrial trans-2-enoyl-CoA reductase
Q9H9J2,MRPL44,mitochondrial ribosomal protein L44
Q6YN16,HSDL2,hydroxysteroid dehydrogenase like 2
O60783,MRPS14,mitochondrial ribosomal protein S14
Q9NUT2,ABCB8,"ATP-binding cassette, sub-family B (MDR/TAP), member 8"
Q8N5M1,ATPAF2,ATP synthase mitochondrial F1 complex assembly factor 2
Q16795,NDUFA9,"NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa"
Q5JTJ3,COA6,cytochrome c oxidase assembly factor 6 homolog (S. cerevisiae)
O00411,POLRMT,polymerase (RNA) mitochondrial (DNA directed)
Q9H1K1,ISCU,iron-sulfur cluster assembly enzyme
Q8WWV3,RTN4IP1,reticulon 4 interacting protein 1
Q9ULD0,OGDHL,oxoglutarate dehydrogenase-like
P36542,ATP5C1,"ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1"
O14874,BCKDK,branched chain ketoacid dehydrogenase kinase
Q969S9,GFM2,"G elongation factor, mitochondrial 2"
Q9P032,NDUFAF4,"NADH dehydrogenase (ubiquinone) complex I, assembly factor 4"
Q3KQZ1,SLC25A35,"solute carrier family 25, member 35"
Q02978,SLC25A11,"solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11"
Q9Y5J9,TIMM8B,translocase of inner mitochondrial membrane 8 homolog B (yeast)
Q8IVS2,MCAT,malonyl CoA:ACP acyltransferase (mitochondrial)
Q5T440,IBA57,"IBA57, iron-sulfur cluster assembly homolog (S. cerevisiae)"
Q99623,PHB2,prohibitin 2
P51398,DAP3,death associated protein 3
Q9NRP2,CMC2,C-x(9)-C motif containing 2
A6NFY7,SDHAF1,succinate dehydrogenase complex assembly factor 1
Q9Y2R5,MRPS17,mitochondrial ribosomal protein S17
Q8IWW8,ADHFE1,"alcohol dehydrogenase, iron containing, 1"
Q9Y697,NFS1,NFS1 cysteine desulfurase
Q5TEU4,NDUFAF5,"NADH dehydrogenase (ubiquinone) complex I, assembly factor 5"
Q9NRX2,MRPL17,mitochondrial ribosomal protein L17
Q9BSH4,TACO1,translational activator of mitochondrially encoded cytochrome c oxidase I
Q8IWA4,MFN1,mitofusin 1
Q8NI37,PPTC7,PTC7 protein phosphatase homolog (S. cerevisiae)
Q9Y3B7,MRPL11,mitochondrial ribosomal protein L11
P13073,COX4I1,cytochrome c oxidase subunit IV isoform 1
O75380,NDUFS6,"NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase)"
Q9BYD1,MRPL13,mitochondrial ribosomal protein L13
P55809,OXCT1,3-oxoacid CoA transferase 1
P10606,COX5B,cytochrome c oxidase subunit Vb
Q15119,PDK2,"pyruvate dehydrogenase kinase, isozyme 2"
P13196,ALAS1,"aminolevulinate, delta-, synthase 1"
O75394,MRPL33,mitochondrial ribosomal protein L33
Q9Y2Z2,MTO1,mitochondrial tRNA translation optimization 1
O43766,LIAS,lipoic acid synthetase
Q16718,NDUFA5,"NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5"
O95139,NDUFB6,"NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa"
O75431,MTX2,metaxin 2
Q96I99,SUCLG2,"succinate-CoA ligase, GDP-forming, beta subunit"
P10109,FDX1,ferredoxin 1
P53007,SLC25A1,"solute carrier family 25 (mitochondrial carrier; citrate transporter), member 1"
Q9Y2Q9,MRPS28,mitochondrial ribosomal protein S28
Q3ZCQ8,TIMM50,translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae)
P45880,VDAC2,voltage-dependent anion channel 2
Q86VD7,SLC25A42,"solute carrier family 25, member 42"
Q9P0U1,TOMM7,translocase of outer mitochondrial membrane 7 homolog (yeast)
Q13011,ECH1,"enoyl CoA hydratase 1, peroxisomal"
O75879,PET112,PET112 homolog (yeast)
Q9Y276,BCS1L,BC1 (ubiquinol-cytochrome c reductase) synthesis-like
O75616,ERAL1,Era-like 12S mitochondrial rRNA chaperone 1
Q7Z7K0,CMC1,C-x(9)-C motif containing 1
Q13084,MRPL28,mitochondrial ribosomal protein L28
P43897,TSFM,"Ts translation elongation factor, mitochondrial"
Q16595,FXN,frataxin
Q9UMS0,NFU1,NFU1 iron-sulfur cluster scaffold homolog (S. cerevisiae)
Q9Y2Z4,YARS2,"tyrosyl-tRNA synthetase 2, mitochondrial"
Q7Z2W9,MRPL21,mitochondrial ribosomal protein L21
P30038,ALDH4A1,"aldehyde dehydrogenase 4 family, member A1"
Q969M1,TOMM40L,translocase of outer mitochondrial membrane 40 homolog (yeast)-like
Q9Y375,NDUFAF1,"NADH dehydrogenase (ubiquinone) complex I, assembly factor 1"
O96000,NDUFB10,"NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa"
P45954,ACADSB,"acyl-CoA dehydrogenase, short/branched chain"
P82933,MRPS9,mitochondrial ribosomal protein S9
Q8NI60,ADCK3,aarF domain containing kinase 3
P49748,ACADVL,"acyl-CoA dehydrogenase, very long chain"
Q9Y3A0,COQ4,coenzyme Q4
Q9P015,MRPL15,mitochondrial ribosomal protein L15
O43678,NDUFA2,"NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa"
Q96A35,MRPL24,mitochondrial ribosomal protein L24
P10809,HSPD1,heat shock 60kDa protein 1 (chaperonin)
O43920,NDUFS5,"NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase)"
Q9UIJ7,AK3,adenylate kinase 3
P99999,CYCS,"cytochrome c, somatic"
Q99797,MIPEP,mitochondrial intermediate peptidase
Q5U5X0,LYRM7,LYR motif containing 7
P43155,CRAT,carnitine O-acetyltransferase
P05166,PCCB,"propionyl CoA carboxylase, beta polypeptide"
Q9Y2R9,MRPS7,mitochondrial ribosomal protein S7
P09001,MRPL3,mitochondrial ribosomal protein L3
O43272,PRODH,proline dehydrogenase (oxidase) 1
P05165,PCCA,"propionyl CoA carboxylase, alpha polypeptide"
Q96RQ3,MCCC1,methylcrotonoyl-CoA carboxylase 1 (alpha)
O15235,MRPS12,mitochondrial ribosomal protein S12
Q9H078,CLPB,ClpB caseinolytic peptidase B homolog (E. coli)
Q15118,PDK1,"pyruvate dehydrogenase kinase, isozyme 1"
Q13405,MRPL49,mitochondrial ribosomal protein L49
P14406,COX7A2,cytochrome c oxidase subunit VIIa polypeptide 2 (liver)
Q9H061,TMEM126A,transmembrane protein 126A
Q86YB7,ECHDC2,enoyl CoA hydratase domain containing 2
P53701,HCCS,holocytochrome c synthase
P31937,HIBADH,3-hydroxyisobutyrate dehydrogenase
P49406,MRPL19,mitochondrial ribosomal protein L19
Q9P0J6,MRPL36,mitochondrial ribosomal protein L36
Q5SVS4,SLC25A30,"solute carrier family 25, member 30"
Q02338,BDH1,"3-hydroxybutyrate dehydrogenase, type 1"
O95363,FARS2,"phenylalanyl-tRNA synthetase 2, mitochondrial"
O75027,ABCB7,"ATP-binding cassette, sub-family B (MDR/TAP), member 7"
Q13505,MTX1,metaxin 1
O95182,NDUFA7,"NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 7, 14.5kDa"
Q99595,TIMM17A,translocase of inner mitochondrial membrane 17 homolog A (yeast)
P49189,ALDH9A1,"aldehyde dehydrogenase 9 family, member A1"
Q9Y3D5,MRPS18C,mitochondrial ribosomal protein S18C
Q96GW9,MARS2,"methionyl-tRNA synthetase 2, mitochondrial"
Q02252,ALDH6A1,"aldehyde dehydrogenase 6 family, member A1"
P22570,FDXR,ferredoxin reductase
O43716,GATC,"glutamyl-tRNA(Gln) amidotransferase, subunit C"
Q12931,TRAP1,TNF receptor-associated protein 1
Q9UKU7,ACAD8,"acyl-CoA dehydrogenase family, member 8"
P05091,ALDH2,aldehyde dehydrogenase 2 family (mitochondrial)
P30405,PPIF,peptidylprolyl isomerase F
Q9Y584,TIMM22,translocase of inner mitochondrial membrane 22 homolog (yeast)
P26440,IVD,isovaleryl-CoA dehydrogenase
Q9H9P8,L2HGDH,L-2-hydroxyglutarate dehydrogenase
O95571,ETHE1,ethylmalonic encephalopathy 1
Q9BYC9,MRPL20,mitochondrial ribosomal protein L20
P05141,SLC25A5,"solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 5"
O75746,SLC25A12,"solute carrier family 25 (aspartate/glutamate carrier), member 12"
P82921,MRPS21,mitochondrial ribosomal protein S21
Q9NS69,TOMM22,translocase of outer mitochondrial membrane 22 homolog (yeast)
P42765,ACAA2,acetyl-CoA acyltransferase 2
Q8TCC3,MRPL30,mitochondrial ribosomal protein L30
Q96EY1,DNAJA3,"DnaJ (Hsp40) homolog, subfamily A, member 3"
O95178,NDUFB2,"NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa"
P82930,MRPS34,mitochondrial ribosomal protein S34
P38117,ETFB,"electron-transfer-flavoprotein, beta polypeptide"
Q8WV93,LACE1,lactation elevated 1
Q9UII2,ATPIF1,ATPase inhibitory factor 1
P24539,ATP5F1,"ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1"
P15954,COX7C,cytochrome c oxidase subunit VIIc
Q9NX63,CHCHD3,coiled-coil-helix-coiled-coil-helix domain containing 3
Q9H8M1,COQ10B,coenzyme Q10 homolog B (S. cerevisiae)
Q4G176,ACSF3,acyl-CoA synthetase family member 3
Q9Y2S7,POLDIP2,"polymerase (DNA-directed), delta interacting protein 2"
Q9UBX3,SLC25A10,"solute carrier family 25 (mitochondrial carrier; dicarboxylate transporter), member 10"
Q9UJS0,SLC25A13,"solute carrier family 25 (aspartate/glutamate carrier), member 13"
Q15120,PDK3,"pyruvate dehydrogenase kinase, isozyme 3"
Q16798,ME3,"malic enzyme 3, NADP(+)-dependent, mitochondrial"
Q9NWU5,MRPL22,mitochondrial ribosomal protein L22
P48735,IDH2,"isocitrate dehydrogenase 2 (NADP+), mitochondrial"
Q92947,GCDH,glutaryl-CoA dehydrogenase
Q9HD33,MRPL47,mitochondrial ribosomal protein L47
Q9H2U2,PPA2,pyrophosphatase (inorganic) 2
Q9BYD2,MRPL9,mitochondrial ribosomal protein L9
Q8WYQ3,CHCHD10,coiled-coil-helix-coiled-coil-helix domain containing 10
Q9UGM6,WARS2,"tryptophanyl tRNA synthetase 2, mitochondrial"
Q9HC21,SLC25A19,"solute carrier family 25 (mitochondrial thiamine pyrophosphate carrier), member 19"
Q8N4T8,CBR4,carbonyl reductase 4
Q9H4I9,SMDT1,single-pass membrane protein with aspartate-rich tail 1
Q16775,HAGH,hydroxyacylglutathione hydrolase
P24310,COX7A1,cytochrome c oxidase subunit VIIa polypeptide 1 (muscle)
Q9BT17,MTG1,mitochondrial ribosome-associated GTPase 1
Q96I36,COX14,cytochrome c oxidase assembly homolog 14 (S. cerevisiae)
Q9UI09,NDUFA12,"NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12"
Q9Y3D3,MRPS16,mitochondrial ribosomal protein S16
Q49AM1,MTERFD3,MTERF domain containing 3
Q6IPR1,LYRM5,LYR motif containing 5
P43304,GPD2,glycerol-3-phosphate dehydrogenase 2 (mitochondrial)
O95299,NDUFA10,"NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa"
O95298,NDUFC2,"NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa"
Q9GZT3,SLIRP,SRA stem-loop interacting RNA binding protein
P00846,ATP6,ATP synthase F0 subunit 6
P00403,COX2,cytochrome c oxidase subunit II
Q9BVV7,TIMM21,translocase of inner mitochondrial membrane 21 homolog (yeast)
P51970,NDUFA8,"NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa"
O94925,GLS,glutaminase
Q9NX14,NDUFB11,"NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa"
Q96HY7,DHTKD1,dehydrogenase E1 and transketolase domain containing 1
Q96GK7,FAHD2A,fumarylacetoacetate hydrolase domain containing 2A
Q92506,HSD17B8,hydroxysteroid (17-beta) dehydrogenase 8
Q9BX68,HINT2,histidine triad nucleotide binding protein 2
P82675,MRPS5,mitochondrial ribosomal protein S5
Q5SQH8,C6orf136,chromosome 6 open reading frame 136
Q8WW59,SPRYD4,SPRY domain containing 4
A6NK58,LIPT2,lipoyl(octanoyl) transferase 2 (putative)
Q16698,DECR1,"2,4-dienoyl CoA reductase 1, mitochondrial"
Q9BYN8,MRPS26,mitochondrial ribosomal protein S26
Q9Y619,SLC25A15,solute carrier family 25 (mitochondrial carrier; ornithine transporter) member 15
P56181,NDUFV3,"NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa"
Q86WA6,BPHL,biphenyl hydrolase-like (serine hydrolase)
Q9UJZ1,STOML2,stomatin (EPB72)-like 2
Q9Y3D2,MSRB2,methionine sulfoxide reductase B2
P83111,LACTB,"lactamase, beta"
O96008,TOMM40,translocase of outer mitochondrial membrane 40 homolog (yeast)
Q6KCM7,SLC25A25,"solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 25"
Q3MIX3,ADCK5,aarF domain containing kinase 5
Q6JQN1,ACAD10,"acyl-CoA dehydrogenase family, member 10"
A3KMH1,VWA8,von Willebrand factor A domain containing 8
Q9GZT6,CCDC90B,coiled-coil domain containing 90B
Q9NVH1,DNAJC11,"DnaJ (Hsp40) homolog, subfamily C, member 11"
Q9BT30,ALKBH7,"alkB, alkylation repair homolog 7 (E. coli)"
P23378,GLDC,glycine dehydrogenase (decarboxylating)
P0DKB6,MPC1L,mitochondrial pyruvate carrier 1-like
Q5T1C6,THEM4,thioesterase superfamily member 4
Q04837,SSBP1,"single-stranded DNA binding protein 1, mitochondrial"
Q9P0M9,MRPL27,mitochondrial ribosomal protein L27
Q8IWL3,HSCB,HscB mitochondrial iron-sulfur cluster co-chaperone
P82664,MRPS10,mitochondrial ribosomal protein S10
P27144,AK4,adenylate kinase 4
Q9NVI7,ATAD3A,"ATPase family, AAA domain containing 3A"
Q9BZE1,MRPL37,mitochondrial ribosomal protein L37
Q9H7Z7,PTGES2,prostaglandin E synthase 2
Q9NNW7,TXNRD2,thioredoxin reductase 2
Q6NUN0,ACSM5,acyl-CoA synthetase medium-chain family member 5
Q9NZ45,CISD1,CDGSH iron sulfur domain 1
Q8IXM3,MRPL41,mitochondrial ribosomal protein L41
Q969Z3,2-Mar,mitochondrial amidoxime reducing component 2
P82932,MRPS6,mitochondrial ribosomal protein S6
Q16540,MRPL23,mitochondrial ribosomal protein L23
Q9Y6N5,SQRDL,sulfide quinone reductase-like (yeast)
O75880,SCO1,SCO1 cytochrome c oxidase assembly protein
O75600,GCAT,glycine C-acetyltransferase
Q6UB35,MTHFD1L,methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 1-like
O75521,ECI2,enoyl-CoA delta isomerase 2
P14927,UQCRB,ubiquinol-cytochrome c reductase binding protein
O75947,ATP5H,"ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d"
O75964,ATP5L,"ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G"
Q4VC31,CCDC58,coiled-coil domain containing 58
Q9HCC0,MCCC2,methylcrotonoyl-CoA carboxylase 2 (beta)
Q96PE7,MCEE,methylmalonyl CoA epimerase
Q9NZB8,MOCS1,molybdenum cofactor synthesis 1
P22033,MUT,methylmalonyl CoA mutase
Q9H1U9,SLC25A51,"solute carrier family 25, member 51"
Q9UQ90,SPG7,spastic paraplegia 7 (pure and complicated autosomal recessive)
P48201,ATP5G3,"ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9)"
Q8NBU5,ATAD1,"ATPase family, AAA domain containing 1"
Q96HP4,OXNAD1,oxidoreductase NAD-binding domain containing 1
Q9H4K7,MTG2,mitochondrial ribosome-associated GTPase 2
Q6PI48,DARS2,"aspartyl-tRNA synthetase 2, mitochondrial"
Q4U2R6,MRPL51,mitochondrial ribosomal protein L51
P11498,PC,pyruvate carboxylase
Q8N0X4,CLYBL,citrate lyase beta like
Q9NP80,PNPLA8,patatin-like phospholipase domain containing 8
O95822,MLYCD,malonyl-CoA decarboxylase
Q96I23,PYURF,PIGY upstream reading frame
O60830,TIMM17B,translocase of inner mitochondrial membrane 17 homolog B (yeast)
Q9BYC8,MRPL32,mitochondrial ribosomal protein L32
Q70HW3,SLC25A26,"solute carrier family 25 (S-adenosylmethionine carrier), member 26"
Q9UF12,PRODH2,proline dehydrogenase (oxidase) 2
Q9NQR4,NIT2,"nitrilase family, member 2"
Q6P4F2,FDX1L,ferredoxin 1-like
P23368,ME2,"malic enzyme 2, NAD(+)-dependent, mitochondrial"
P49411,TUFM,"Tu translation elongation factor, mitochondrial"
Q02221,COX6A2,cytochrome c oxidase subunit VIa polypeptide 2
Q6PML9,SLC30A9,"solute carrier family 30 (zinc transporter), member 9"
Q96BW9,TAMM41,"TAM41, mitochondrial translocator assembly and maintenance protein, homolog (S. cerevisiae)"
O14925,TIMM23,translocase of inner mitochondrial membrane 23 homolog (yeast)
Q9NWS8,RMND1,required for meiotic nuclear division 1 homolog (S. cerevisiae)
O95140,MFN2,mitofusin 2
Q5SXM8,DNLZ,DNL-type zinc finger
Q8N4Q1,CHCHD4,coiled-coil-helix-coiled-coil-helix domain containing 4
O14561,NDUFAB1,"NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa"
Q08AH1,ACSM1,acyl-CoA synthetase medium-chain family member 1
Q86WW8,COA5,cytochrome c oxidase assembly factor 5
Q96H96,COQ2,coenzyme Q2 4-hydroxybenzoate polyprenyltransferase
Q86YH6,PDSS2,"prenyl (decaprenyl) diphosphate synthase, subunit 2"
Q08426,EHHADH,"enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase"
O75489,NDUFS3,"NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase)"
Q9NRK6,ABCB10,"ATP-binding cassette, sub-family B (MDR/TAP), member 10"
P17540,CKMT2,"creatine kinase, mitochondrial 2 (sarcomeric)"
P82663,MRPS25,mitochondrial ribosomal protein S25
Q9H845,ACAD9,"acyl-CoA dehydrogenase family, member 9"
Q9P0S2,COX16,COX16 cytochrome c oxidase assembly homolog (S. cerevisiae)
Q96ND0,FAM210A,"family with sequence similarity 210, member A"
Q9NPJ3,ACOT13,acyl-CoA thioesterase 13
P50416,CPT1A,carnitine palmitoyltransferase 1A (liver)
P32189,GK,glycerol kinase
Q9BTZ2,DHRS4,dehydrogenase/reductase (SDR family) member 4
Q8N945,PRELID2,PRELI domain containing 2
Q9HA77,CARS2,"cysteinyl-tRNA synthetase 2, mitochondrial (putative)"
O75323,GBAS,glioblastoma amplified sequence
P17568,NDUFB7,"NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa"
Q5XKP0,C19orf70,chromosome 19 open reading frame 70
Q9NS18,GLRX2,glutaredoxin 2
Q9NP92,MRPS30,mitochondrial ribosomal protein S30
O43819,SCO2,SCO2 cytochrome c oxidase assembly protein
Q99714,HSD17B10,hydroxysteroid (17-beta) dehydrogenase 10
Q96I59,NARS2,"asparaginyl-tRNA synthetase 2, mitochondrial (putative)"
Q6P087,RPUSD3,RNA pseudouridylate synthase domain containing 3
P51687,SUOX,sulfite oxidase
Q9UL12,SARDH,sarcosine dehydrogenase
P52758,HRSP12,heat-responsive protein 12
P10176,COX8A,cytochrome c oxidase subunit VIIIA (ubiquitous)
P35270,SPR,"sepiapterin reductase (7,8-dihydrobiopterin:NADP+ oxidoreductase)"
P39210,MPV17,MpV17 mitochondrial inner membrane protein
Q8N4Q0,ZADH2,zinc binding alcohol dehydrogenase domain containing 2
Q9H0U6,MRPL18,mitochondrial ribosomal protein L18
P30837,ALDH1B1,"aldehyde dehydrogenase 1 family, member B1"
Q96BP2,CHCHD1,coiled-coil-helix-coiled-coil-helix domain containing 1
O60220,TIMM8A,translocase of inner mitochondrial membrane 8 homolog A (yeast)
Q9Y277,VDAC3,voltage-dependent anion channel 3
Q6NUK1,SLC25A24,"solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 24"
Q9Y5U8,MPC1,mitochondrial pyruvate carrier 1
Q9H936,SLC25A22,"solute carrier family 25 (mitochondrial carrier: glutamate), member 22"
Q9H0C2,SLC25A31,"solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 31"
Q9H1K4,SLC25A18,"solute carrier family 25 (glutamate carrier), member 18"
Q96Q11,TRNT1,"tRNA nucleotidyl transferase, CCA-adding, 1"
P14735,IDE,insulin-degrading enzyme
Q9Y2Q3,GSTK1,glutathione S-transferase kappa 1
Q5ST30,VARS2,"valyl-tRNA synthetase 2, mitochondrial"
P61604,HSPE1,heat shock 10kDa protein 1
Q6P161,MRPL54,mitochondrial ribosomal protein L54
Q96DV4,MRPL38,mitochondrial ribosomal protein L38
Q14197,ICT1,immature colon carcinoma transcript 1
Q9NZJ7,MTCH1,mitochondrial carrier 1
O43715,TRIAP1,TP53 regulated inhibitor of apoptosis 1
Q96EY7,PTCD3,pentatricopeptide repeat domain 3
Q12887,COX10,cytochrome c oxidase assembly homolog 10 (yeast)
Q92667,AKAP1,A kinase (PRKA) anchor protein 1
Q9HC36,RNMTL1,RNA methyltransferase like 1
P54819,AK2,adenylate kinase 2
Q9BUB7,TMEM70,transmembrane protein 70
Q8NC60,NOA1,nitric oxide associated 1
Q96AQ8,MCUR1,mitochondrial calcium uniporter regulator 1
Q9P0S9,TMEM14C,transmembrane protein 14C
O43677,NDUFC1,"NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa"
Q9NZE8,MRPL35,mitochondrial ribosomal protein L35
O95167,NDUFA3,"NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa"
Q5T2R2,PDSS1,"prenyl (decaprenyl) diphosphate synthase, subunit 1"
P16260,SLC25A16,"solute carrier family 25 (mitochondrial carrier; Graves disease autoantigen), member 16"
FMC1,C7orf55,chromosome 7 open reading frame 55
Q53FZ2,ACSM3,acyl-CoA synthetase medium-chain family member 3
Q330K2,NDUFAF6,"NADH dehydrogenase (ubiquinone) complex I, assembly factor 6"
P25874,UCP1,"uncoupling protein 1 (mitochondrial, proton carrier)"
Q9H9B4,SFXN1,sideroflexin 1
Q86SX6,GLRX5,glutaredoxin 5
Q86Y79,PTRH1,peptidyl-tRNA hydrolase 1 homolog (S. cerevisiae)
P82912,MRPS11,mitochondrial ribosomal protein S11
Q9NQH7,XPNPEP3,"X-prolyl aminopeptidase (aminopeptidase P) 3, putative"
Q9P0J1,PDP1,pyruvate dehyrogenase phosphatase catalytic subunit 1
P42126,ECI1,enoyl-CoA delta isomerase 1
Q9BQT8,SLC25A21,"solute carrier family 25 (mitochondrial oxoadipate carrier), member 21"
Q8N8R3,SLC25A29,"solute carrier family 25 (mitochondrial carnitine/acylcarnitine carrier), member 29"
Q8N413,SLC25A45,"solute carrier family 25, member 45"
Q9NRP4,ACN9,ACN9 homolog (S. cerevisiae)
Q9Y3B1,SLMO2,slowmo homolog 2 (Drosophila)
Q9BZJ4,SLC25A39,"solute carrier family 25, member 39"
O43676,NDUFB3,"NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa"
Q9Y3B8,REXO2,RNA exonuclease 2
P50440,GATM,glycine amidinotransferase (L-arginine:glycine amidinotransferase)
Q9Y5J6,TIMM10B,translocase of inner mitochondrial membrane 10 homolog B (yeast)
Q9NP81,SARS2,"seryl-tRNA synthetase 2, mitochondrial"
Q8NE62,CHDH,choline dehydrogenase
Q9BQC6,MRPL57,mitochondrial ribosomal protein L57
Q6P1X6,C8orf82,chromosome 8 open reading frame 82
Q5JPH6,EARS2,"glutamyl-tRNA synthetase 2, mitochondrial"
Q9UBQ7,GRHPR,glyoxylate reductase/hydroxypyruvate reductase
Q96DP5,MTFMT,mitochondrial methionyl-tRNA formyltransferase
Q8WV60,PTCD2,pentatricopeptide repeat domain 2
Q9NTX5,ECHDC1,enoyl CoA hydratase domain containing 1
P49590,HARS2,"histidyl-tRNA synthetase 2, mitochondrial"
O00483,NDUFA4,"NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa"
Q9P0J0,NDUFA13,"NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 13"
Q8NCW5,APOA1BP,apolipoprotein A-I binding protein
P17152,TMEM11,transmembrane protein 11
Q9BVL4,SELO,selenoprotein O
Q8N159,NAGS,N-acetylglutamate synthase
P51659,HSD17B4,hydroxysteroid (17-beta) dehydrogenase 4
Q7L592,NDUFAF7,"NADH dehydrogenase (ubiquinone) complex I, assembly factor 7"
P04181,OAT,ornithine aminotransferase
Q8N5N7,MRPL50,mitochondrial ribosomal protein L50
P24311,COX7B,cytochrome c oxidase subunit VIIb
Q5T160,RARS2,"arginyl-tRNA synthetase 2, mitochondrial"
Q5BKU9,OXLD1,oxidoreductase-like domain containing 1
Q53H82,LACTB2,"lactamase, beta 2"
Q86Y39,NDUFA11,"NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 11, 14.7kDa"
Q9NWT8,AURKAIP1,aurora kinase A interacting protein 1
Q9BUK0,CHCHD7,coiled-coil-helix-coiled-coil-helix domain containing 7
P34897,SHMT2,serine hydroxymethyltransferase 2 (mitochondrial)
P13995,MTHFD2,"methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 2, methenyltetrahydrofolate cyclohydrolase"
Q96DB5,RMDN1,regulator of microtubule dynamics 1
P31327,CPS1,"carbamoyl-phosphate synthase 1, mitochondrial"
Q6P1L8,MRPL14,mitochondrial ribosomal protein L14
Q9P0P8,C6orf203,chromosome 6 open reading frame 203
Q8NBN7,RDH13,retinol dehydrogenase 13 (all-trans/9-cis)
Q96GJ1,TRMT2B,tRNA methyltransferase 2 homolog B (S. cerevisiae)
Q96EL2,MRPS24,mitochondrial ribosomal protein S24
Q9Y2R0,COA3,cytochrome c oxidase assembly factor 3
P00390,GSR,glutathione reductase
Q14249,ENDOG,endonuclease G
O15382,BCAT2,"branched chain amino-acid transaminase 2, mitochondrial"
Q96QE5,TEFM,"transcription elongation factor, mitochondrial"
Q96CM8,ACSF2,acyl-CoA synthetase family member 2
O75648,TRMU,tRNA 5-methylaminomethyl-2-thiouridylate methyltransferase
P82650,MRPS22,mitochondrial ribosomal protein S22
P28838,LAP3,leucine aminopeptidase 3
P00367,GLUD1,glutamate dehydrogenase 1
P35914,HMGCL,3-hydroxymethyl-3-methylglutaryl-CoA lyase
P49789,FHIT,fragile histidine triad
Q9Y291,MRPS33,mitochondrial ribosomal protein S33
Q8TB37,NUBPL,nucleotide binding protein-like
Q9NU23,LYRM2,LYR motif containing 2
Q2QL34,MPV17L,MPV17 mitochondrial membrane protein-like
Q8TAE8,GADD45GIP1,"growth arrest and DNA-damage-inducible, gamma interacting protein 1"
Q00059,TFAM,"transcription factor A, mitochondrial"
P54886,ALDH18A1,"aldehyde dehydrogenase 18 family, member A1"
Q9NWU1,OXSM,"3-oxoacyl-ACP synthase, mitochondrial"
Q6YP21,CCBL2,cysteine conjugate-beta lyase 2
Q9BW92,TARS2,"threonyl-tRNA synthetase 2, mitochondrial (putative)"
Q969Z0,TBRG4,transforming growth factor beta regulator 4
Q6PI78,TMEM65,transmembrane protein 65
P60602,ROMO1,reactive oxygen species modulator 1
P30044,PRDX5,peroxiredoxin 5
Q9Y5T4,DNAJC15,"DnaJ (Hsp40) homolog, subfamily C, member 15"
Q8WWC4,C2orf47,chromosome 2 open reading frame 47
Q9Y241,HIGD1A,"HIG1 hypoxia inducible domain family, member 1A"
Q4G0I0,C16orf91,chromosome 16 open reading frame 91
Q8IXI1,RHOT2,ras homolog family member T2
Q96H78,SLC25A44,"solute carrier family 25, member 44"
Q9NYQ3,HAO2,hydroxyacid oxidase 2 (long chain)
Q15070,OXA1L,oxidase (cytochrome c) assembly 1-like
Q96AG3,SLC25A46,"solute carrier family 25, member 46"
Q9HBH5,RDH14,retinol dehydrogenase 14 (all-trans/9-cis/11-cis)
P56378,C14orf2,chromosome 14 open reading frame 2
Q9Y2D0,CA5B,"carbonic anhydrase VB, mitochondrial"
Q13057,COASY,CoA synthase
P0C7P0,CISD3,CDGSH iron sulfur domain 3
O43708,GSTZ1,glutathione S-transferase zeta 1
Q6YFQ2,COX6B2,cytochrome c oxidase subunit VIb polypeptide 2 (testis)
Q9HC38,GLOD4,glyoxalase domain containing 4
P09110,ACAA1,acetyl-CoA acyltransferase 1
Q9UKG9,CROT,carnitine O-octanoyltransferase
Q9HBH1,PDF,peptide deformylase (mitochondrial)
Q49B96,COX19,cytochrome c oxidase assembly homolog 19 (S. cerevisiae)
P48728,AMT,aminomethyltransferase
Q8NCN5,PDPR,pyruvate dehydrogenase phosphatase regulatory subunit
Q9BYT8,NLN,neurolysin (metallopeptidase M3 family)
Q9Y3E2,BOLA1,bolA family member 1
P22557,ALAS2,"aminolevulinate, delta-, synthase 2"
Q8TAA5,GRPEL2,"GrpE-like 2, mitochondrial (E. coli)"
P49419,ALDH7A1,"aldehyde dehydrogenase 7 family, member A1"
Q9BXW7,CECR5,"cat eye syndrome chromosome region, candidate 5"
P55789,GFER,"growth factor, augmenter of liver regeneration"
Q96T52,IMMP2L,IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae)
Q96KJ9,COX4I2,cytochrome c oxidase subunit IV isoform 2 (lung)
Q9NYK5,MRPL39,mitochondrial ribosomal protein L39
Q8N5Z0,AADAT,aminoadipate aminotransferase
Q9BWH2,FUNDC2,FUN14 domain containing 2
O75608,LYPLA1,lysophospholipase I
P29803,PDHA2,pyruvate dehydrogenase (lipoamide) alpha 2
Q9UGC7,MTRF1L,mitochondrial translational release factor 1-like
Q969Y2,GTPBP3,GTP binding protein 3 (mitochondrial)
Q9H903,MTHFD2L,methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 2-like
Q96TA2,YME1L1,YME1-like 1 ATPase
P49753,ACOT2,acyl-CoA thioesterase 2
Q96IL0,APOPT1,"apoptogenic 1, mitochondrial"
Q96EY8,MMAB,methylmalonic aciduria (cobalamin deficiency) cblB type
P50336,PPOX,protoporphyrinogen oxidase
P28288,ABCD3,"ATP-binding cassette, sub-family D (ALD), member 3"
Q9NTG7,SIRT3,sirtuin 3
Q86WU2,LDHD,lactate dehydrogenase D
B4DEF8,MRPL45,mitochondrial ribosomal protein L45
Q9H3J6,C12orf65,chromosome 12 open reading frame 65
Q96LU5,IMMP1L,IMP1 inner mitochondrial membrane peptidase-like (S. cerevisiae)
P54098,POLG,"polymerase (DNA directed), gamma"
Q5TC12,ATPAF1,ATP synthase mitochondrial F1 complex assembly factor 1
P78537,BLOC1S1,"biogenesis of lysosomal organelles complex-1, subunit 1"
Q3SY69,ALDH1L2,"aldehyde dehydrogenase 1 family, member L2"
Q8N8Q8,COX18,COX18 cytochrome C oxidase assembly factor
P36551,CPOX,coproporphyrinogen oxidase
Q13423,NNT,nicotinamide nucleotide transhydrogenase
A1L188,C17orf89,chromosome 17 open reading frame 89
Q9Y6H3,XRCC6BP1,XRCC6 binding protein 1
Q8WVC6,DCAKD,dephospho-CoA kinase domain containing
P56134,ATP5J2,"ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2"
P53985,SLC16A1,"solute carrier family 16 (monocarboxylate transporter), member 1"
Q9BWM7,SFXN3,sideroflexin 3
Q86WA8,LONP2,"lon peptidase 2, peroxisomal"
Q9UDR5,AASS,aminoadipate-semialdehyde synthase
Q9NR28,DIABLO,"diablo, IAP-binding mitochondrial protein"
Q7Z4L0,COX8C,cytochrome c oxidase subunit VIIIC
Q9NR77,PXMP2,"peroxisomal membrane protein 2, 22kDa"
Q9BYV1,AGXT2,alanine--glyoxylate aminotransferase 2
Q9UI32,GLS2,"glutaminase 2 (liver, mitochondrial)"
Q9BUR5,APOO,apolipoprotein O
Q709F0,ACAD11,"acyl-CoA dehydrogenase family, member 11"
A6NC05,C5orf63,chromosome 5 open reading frame 63
Q86XE5,HOGA1,4-hydroxy-2-oxoglutarate aldolase 1
Q6DKK2,TTC19,tetratricopeptide repeat domain 19
Q9NPE2,NGRN,"neugrin, neurite outgrowth associated"
Q8N3R3,TCAIM,"T cell activation inhibitor, mitochondrial"
P23434,GCSH,glycine cleavage system protein H (aminomethyl carrier)
Q9NXA8,SIRT5,sirtuin 5
Q8TD30,GPT2,glutamic pyruvate transaminase (alanine aminotransferase) 2
Q96B49,TOMM6,translocase of outer mitochondrial membrane 6 homolog (yeast)
Q96A26,FAM162A,"family with sequence similarity 162, member A"
Q9NP58,ABCB6,"ATP-binding cassette, sub-family B (MDR/TAP), member 6"
Q9BQ69,MACROD1,MACRO domain containing 1
Q16762,TST,thiosulfate sulfurtransferase (rhodanese)
P00395,COX1,cytochrome c oxidase subunit I
Q9H019,MTFR1L,mitochondrial fission regulator 1-like
Q9NRG7,SDR39U1,"short chain dehydrogenase/reductase family 39U, member 1"
Q9UI17,DMGDH,dimethylglycine dehydrogenase
O95258,SLC25A14,"solute carrier family 25 (mitochondrial carrier, brain), member 14"
Q96N28,SLMO1,slowmo homolog 1 (Drosophila)
O43808,SLC25A17,"solute carrier family 25 (mitochondrial carrier; peroxisomal membrane protein, 34kDa), member 17"
Q9BSY4,CHCHD5,coiled-coil-helix-coiled-coil-helix domain containing 5
O94826,TOMM70A,translocase of outer mitochondrial membrane 70 homolog A (S. cerevisiae)
Q86X76,NIT1,nitrilase 1
Q6P587,FAHD1,fumarylacetoacetate hydrolase domain containing 1
Q8NE86,MCU,mitochondrial calcium uniporter
Q02318,CYP27A1,"cytochrome P450, family 27, subfamily A, polypeptide 1"
P03891,ND2,MTND2
P03905,ND4,"NADH dehydrogenase, subunit 4 (complex I)"
P03915,ND5,"NADH dehydrogenase, subunit 5 (complex I)"
P40925,MDH1,"malate dehydrogenase 1, NAD (soluble)"
Q14154,KIAA0141,KIAA0141
Q53R41,FASTKD1,FAST kinase domains 1
Q92665,MRPS31,mitochondrial ribosomal protein S31
O75891,ALDH1L1,"aldehyde dehydrogenase 1 family, member L1"
O75127,PTCD1,pentatricopeptide repeat domain 1
P55084,HADHB,"hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), beta subunit"
Q9H3H1,TRIT1,tRNA isopentenyltransferase 1
Q9UJA2,CRLS1,cardiolipin synthase 1
Q8IVS8,GLYCTK,glycerate kinase
Q9H2D1,SLC25A32,"solute carrier family 25 (mitochondrial folate carrier), member 32"
Q5JTZ9,AARS2,"alanyl-tRNA synthetase 2, mitochondrial"
Q9Y2C4,EXOG,"endo/exonuclease (5'-3'), endonuclease G-like"
Q9Y6H1,CHCHD2,coiled-coil-helix-coiled-coil-helix domain containing 2
O15229,KMO,kynurenine 3-monooxygenase (kynurenine 3-hydroxylase)
Q8TD22,SFXN5,sideroflexin 5
Q9BQ52,ELAC2,elaC ribonuclease Z 2
P07203,GPX1,glutathione peroxidase 1
Q92523,CPT1B,carnitine palmitoyltransferase 1B (muscle)
P48163,ME1,"malic enzyme 1, NADP(+)-dependent, cytosolic"
Q9Y3D6,FIS1,fission 1 (mitochondrial outer membrane) homolog (S. cerevisiae)
Q9Y255,PRELID1,PRELI domain containing 1
P55916,UCP3,"uncoupling protein 3 (mitochondrial, proton carrier)"
O95847,SLC25A27,"solute carrier family 25, member 27"
Q8TBP6,SLC25A40,"solute carrier family 25, member 40"
Q9BV35,SLC25A23,"solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 23"
Q9Y5R4,HEMK1,HemK methyltransferase family member 1
Q96CQ1,SLC25A36,"solute carrier family 25 (pyrimidine nucleotide carrier ), member 36"
Q96E52,OMA1,OMA1 zinc metallopeptidase
Q2VYF4,LETM2,leucine zipper-EF-hand containing transmembrane protein 2
Q96LJ7,DHRS1,dehydrogenase/reductase (SDR family) member 1
P27105,STOM,stomatin
Q9NRN9,METTL5,methyltransferase like 5
Q9UJ68,MSRA,methionine sulfoxide reductase A
Q8WV74,NUDT8,nudix (nucleoside diphosphate linked moiety X)-type motif 8
Q96T66,NMNAT3,nicotinamide nucleotide adenylyltransferase 3
Q96DW6,SLC25A38,"solute carrier family 25, member 38"
Q567V2,MPV17L2,MPV17 mitochondrial membrane protein-like 2
P53396,ACLY,ATP citrate lyase
Q9UBJ2,ABCD2,"ATP-binding cassette, sub-family D (ALD), member 2"
Q8NFF5,FLAD1,flavin adenine dinucleotide synthetase 1
Q9Y234,LIPT1,lipoyltransferase 1
Q7Z3D6,C14orf159,chromosome 14 open reading frame 159
Q16822,PCK2,phosphoenolpyruvate carboxykinase 2 (mitochondrial)
Q4G0N4,NADK2,"NAD kinase 2, mitochondrial"
P52789,HK2,hexokinase 2
P25325,MPST,mercaptopyruvate sulfurtransferase
Q86X67,NUDT13,nudix (nucleoside diphosphate linked moiety X)-type motif 13
Q13085,ACACA,acetyl-CoA carboxylase alpha
P80404,ABAT,4-aminobutyrate aminotransferase
P54868,HMGCS2,3-hydroxy-3-methylglutaryl-CoA synthase 2 (mitochondrial)
P51649,ALDH5A1,"aldehyde dehydrogenase 5 family, member A1"
CKMT1,CKMT1A,"creatine kinase, mitochondrial 1A"
Q9UG56,PISD,phosphatidylserine decarboxylase
O95168,NDUFB4,"NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa"
O14957,UQCR11,"ubiquinol-cytochrome c reductase, complex III subunit XI"
Q96C01,FAM136A,"family with sequence similarity 136, member A"
Q8N4H5,TOMM5,translocase of outer mitochondrial membrane 5 homolog (yeast)
O43464,HTRA2,HtrA serine peptidase 2
P06744,GPI,glucose-6-phosphate isomerase
O15239,NDUFA1,"NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa"
P00156,CYTB,cytochrome b
Q16774,GUK1,guanylate kinase 1
Q8N465,D2HGDH,D-2-hydroxyglutarate dehydrogenase
Q9H6K4,OPA3,"optic atrophy 3 (autosomal recessive, with chorea and spastic paraplegia)"
O60218,AKR1B10,"aldo-keto reductase family 1, member B10 (aldose reductase)"
O14832,PHYH,phytanoyl-CoA 2-hydroxylase
Q8N183,NDUFAF2,"NADH dehydrogenase (ubiquinone) complex I, assembly factor 2"
Q9BQ95,ECSIT,ECSIT signalling integrator
Q9H300,PARL,"presenilin associated, rhomboid-like"
Q9Y6G3,MRPL42,mitochondrial ribosomal protein L42
Q9NNZ3,DNAJC4,"DnaJ (Hsp40) homolog, subfamily C, member 4"
Q9Y3D7,PAM16,presequence translocase-associated motor 16 homolog (S. cerevisiae)
P51648,ALDH3A2,"aldehyde dehydrogenase 3 family, member A2"
Q9UKU0,ACSL6,acyl-CoA synthetase long-chain family member 6
Q2T9J0,TYSND1,trypsin domain containing 1
Q9HD23,MRS2,MRS2 magnesium transporter
Q9NUJ1,ABHD10,abhydrolase domain containing 10
Q9NQE9,HINT3,histidine triad nucleotide binding protein 3
Q9Y6I8,PXMP4,"peroxisomal membrane protein 4, 24kDa"
Q9H4B0,OSGEPL1,O-sialoglycoprotein endopeptidase-like 1
P50583,NUDT2,nudix (nucleoside diphosphate linked moiety X)-type motif 2
O43169,CYB5B,cytochrome b5 type B (outer mitochondrial membrane)
Q12849,GRSF1,G-rich RNA sequence binding factor 1
Q9Y676,MRPS18B,mitochondrial ribosomal protein S18B
Q96LL9,DNAJC30,"DnaJ (Hsp40) homolog, subfamily C, member 30"
P04040,CAT,catalase
Q16854,DGUOK,deoxyguanosine kinase
Q9Y305,ACOT9,acyl-CoA thioesterase 9
Q9NUB1,ACSS1,acyl-CoA synthetase short-chain family member 1
Q969G6,RFK,riboflavin kinase
Q9NQZ5,STARD7,StAR-related lipid transfer (START) domain containing 7
Q8WUD6,CHPT1,choline phosphotransferase 1
P03928,ATP8,ATP synthase F0 subunit 8
Q9NPL8,TIMMDC1,translocase of inner mitochondrial membrane domain containing 1
Q7Z5L4,SPATA19,spermatogenesis associated 19
Q9BUP3,HTATIP2,"HIV-1 Tat interactive protein 2, 30kDa"
O43488,AKR7A2,"aldo-keto reductase family 7, member A2 (aflatoxin aldehyde reductase)"
P33316,DUT,deoxyuridine triphosphatase
Q14667,KIAA0100,KIAA0100
P00414,COX3,cytochrome c oxidase III
Q6IAN0,DHRS7B,dehydrogenase/reductase (SDR family) member 7B
O75570,MTRF1,mitochondrial translational release factor 1
Q96AN5,TMEM143,transmembrane protein 143
Q9NPB1,NT5M,"5',3'-nucleotidase, mitochondrial"
Q8IXI2,RHOT1,ras homolog family member T1
O00746,NME4,NME/NM23 nucleoside diphosphate kinase 4
P49914,MTHFS,"5,10-methenyltetrahydrofolate synthetase (5-formyltetrahydrofolate cyclo-ligase)"
Q9BSF4,C19orf52,chromosome 19 open reading frame 52
Q9NVS9,PNPO,pyridoxamine 5'-phosphate oxidase
O75874,IDH1,"isocitrate dehydrogenase 1 (NADP+), soluble"
Q8IYU8,MICU2,mitochondrial calcium uptake 2
Q9H0N5,PCBD2,pterin-4 alpha-carbinolamine dehydratase/dimerization cofactor of hepatocyte nuclear factor 1 alpha (TCF1) 2
Q9H0R6,QRSL1,glutaminyl-tRNA synthase (glutamine-hydrolyzing)-like 1
Q86TW2,ADCK1,aarF domain containing kinase 1
P30041,PRDX6,peroxiredoxin 6
P29401,TKT,transketolase
Q9BPW8,NIPSNAP1,nipsnap homolog 1 (C. elegans)
P41250,GARS,glycyl-tRNA synthetase
Q08AH3,ACSM2A,acyl-CoA synthetase medium-chain family member 2A
Q9BSK2,SLC25A33,"solute carrier family 25 (pyrimidine nucleotide carrier), member 33"
Q8N5I4,DHRSX,dehydrogenase/reductase (SDR family) X-linked
A8MSI8,LYRM9,LYR motif containing 9
Q969Q5,RAB24,"RAB24, member RAS oncogene family"
Q7L3T8,PARS2,"prolyl-tRNA synthetase 2, mitochondrial (putative)"
Q86TS9,MRPL52,mitochondrial ribosomal protein L52
Q9Y606,PUS1,pseudouridylate synthase 1
P00505,GOT2,"glutamic-oxaloacetic transaminase 2, mitochondrial"
Q8IW45,CARKD,carbohydrate kinase domain containing
P03897,ND3,"NADH dehydrogenase, subunit 3 (complex I)"
Q96QU6,ACCS,1-aminocyclopropane-1-carboxylate synthase homolog (Arabidopsis)(non-functional)
Q9Y3E5,PTRH2,peptidyl-tRNA hydrolase 2
Q32NB8,PGS1,phosphatidylglycerophosphate synthase 1
Q8N573,OXR1,oxidation resistance 1
Q5VWZ2,LYPLAL1,lysophospholipase-like 1
Q9NX36,DNAJC28,"DnaJ (Hsp40) homolog, subfamily C, member 28"
P78417,GSTO1,glutathione S-transferase omega 1
Q05932,FPGS,folylpolyglutamate synthase
Q6UW68,TMEM205,transmembrane protein 205
Q5H9E4,SLC25A53,"solute carrier family 25, member 53"
Q96NN9,AIFM3,"apoptosis-inducing factor, mitochondrion-associated, 3"
P10620,MGST1,microsomal glutathione S-transferase 1
Q86UQ4,ABCA13,"ATP-binding cassette, sub-family A (ABC1), member 13"
Q9UDX5,MTFP1,mitochondrial fission process 1
Q13509,TUBB3,"tubulin, beta 3 class III"
Q9NYJ1,COA4,cytochrome c oxidase assembly factor 4 homolog (S. cerevisiae)
Q9GZT8,NIF3L1,NIF3 NGG1 interacting factor 3-like 1 (S. cerevisiae)
Q8N0Z8,PUSL1,pseudouridylate synthase-like 1
Q96GA7,SDSL,serine dehydratase-like
Q07812,BAX,BCL2-associated X protein
Q7Z434,MAVS,mitochondrial antiviral signaling protein
Q9H7H0,METTL17,methyltransferase like 17
O00763,ACACB,acetyl-CoA carboxylase beta
P78540,ARG2,arginase 2
Q9NVV4,MTPAP,mitochondrial poly(A) polymerase
Q96ER9,CCDC51,coiled-coil domain containing 51
Q9HAC7,SUGCT,succinylCoA:glutarate-CoA transferase
O00429,DNM1L,dynamin 1-like
O43847,NRD1,nardilysin (N-arginine dibasic convertase)
Q8IUX1,TMEM126B,transmembrane protein 126B
Q96CB9,NSUN4,"NOP2/Sun domain family, member 4"
Q9H6R3,ACSS3,acyl-CoA synthetase short-chain family member 3
Q96KR6,FAM210B,"family with sequence similarity 210, member B"
Q8N0V3,RBFA,ribosome binding factor A (putative)
Q8N5K1,CISD2,CDGSH iron sulfur domain 2
Q6UB28,METAP1D,methionyl aminopeptidase type 1D (mitochondrial)
O43865,AHCYL1,adenosylhomocysteinase-like 1
Q9UFN0,NIPSNAP3A,nipsnap homolog 3A (C. elegans)
Q5VT66,1-Mar,mitochondrial amidoxime reducing component 1
Q8IVP5,FUNDC1,FUN14 domain containing 1
P33121,ACSL1,acyl-CoA synthetase long-chain family member 1
Q5RI15,COX20,COX20 cytochrome C oxidase assembly factor
Q3SXM5,HSDL1,hydroxysteroid dehydrogenase like 1
O75828,CBR3,carbonyl reductase 3
Q7Z6M4,MTERFD2,MTERF domain containing 2
A8MXV4,NUDT19,nudix (nucleoside diphosphate linked moiety X)-type motif 19
Q9NRV9,HEBP1,heme binding protein 1
Q8WUK0,PTPMT1,"protein tyrosine phosphatase, mitochondrial 1"
Q96HS1,PGAM5,phosphoglycerate mutase family member 5
P23919,DTYMK,deoxythymidylate kinase (thymidylate kinase)
Q15046,KARS,lysyl-tRNA synthetase
P49675,STAR,steroidogenic acute regulatory protein
Q96DA6,DNAJC19,"DnaJ (Hsp40) homolog, subfamily C, member 19"
P08397,HMBS,hydroxymethylbilane synthase
P00480,OTC,ornithine carbamoyltransferase
O14548,COX7A2L,cytochrome c oxidase subunit VIIa polypeptide 2 like
Q96E29,MTERFD1,MTERF domain containing 1
Q96NB2,SFXN2,sideroflexin 2
P49327,FASN,fatty acid synthase
Q9BXM7,PINK1,PTEN induced putative kinase 1
Q53S58,TMEM177,transmembrane protein 177
Q16881,TXNRD1,thioredoxin reductase 1
Q8IYQ7,THNSL1,threonine synthase-like 1 (S. cerevisiae)
O43826,SLC37A4,"solute carrier family 37 (glucose-6-phosphate transporter), member 4"
P14324,FDPS,farnesyl diphosphate synthase
Q13907,IDI1,isopentenyl-diphosphate delta isomerase 1
Q13472,TOP3A,topoisomerase (DNA) III alpha
Q8N4E7,FTMT,ferritin mitochondrial
Q9BYZ2,LDHAL6B,lactate dehydrogenase A-like 6B
Q99700,ATXN2,ataxin 2
Q15390,MTFR1,mitochondrial fission regulator 1
O94760,DDAH1,dimethylarginine dimethylaminohydrolase 1
Q9BXK5,BCL2L13,BCL2-like 13 (apoptosis facilitator)
Q7L0Y3,TRMT10C,tRNA methyltransferase 10 homolog C (S. cerevisiae)
O00154,ACOT7,acyl-CoA thioesterase 7
Q8WVM0,TFB1M,"transcription factor B1, mitochondrial"
P84085,ARF5,ADP-ribosylation factor 5
Q9NWR8,CCDC109B,coiled-coil domain containing 109B
Q96RR1,C10orf2,chromosome 10 open reading frame 2
Q9H3L0,MMADHC,"methylmalonic aciduria (cobalamin deficiency) cblD type, with homocystinuria"
Q96Q83,ALKBH3,"alkB, alkylation repair homolog 3 (E. coli)"
Q96C36,PYCR2,"pyrroline-5-carboxylate reductase family, member 2"
P62269,RPS18,ribosomal protein S18
Q8NFU3,TSTD1,thiosulfate sulfurtransferase (rhodanese)-like domain containing 1
Q8TC12,RDH11,retinol dehydrogenase 11 (all-trans/9-cis/11-cis)
Q9UBY9,HSPB7,"heat shock 27kDa protein family, member 7 (cardiovascular)"
O43325,LYRM1,LYR motif containing 1
Q9BXW6,OSBPL1A,oxysterol binding protein-like 1A
O94761,RECQL4,RecQ protein-like 4
P0DJ07,PET100,PET100 homolog (S. cerevisiae)
P19367,HK1,hexokinase 1
Q8TB36,GDAP1,ganglioside induced differentiation associated protein 1
Q9H2K0,MTIF3,mitochondrial translational initiation factor 3
P13051,UNG,uracil-DNA glycosylase
Q6IB77,GLYAT,glycine-N-acyltransferase
P34896,SHMT1,serine hydroxymethyltransferase 1 (soluble)
Q96AB3,ISOC2,isochorismatase domain containing 2
Q03393,PTS,6-pyruvoyltetrahydropterin synthase
Q96BP3,PPWD1,peptidylprolyl isomerase domain and WD repeat containing 1
P05496,ATP5G1,"ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9)"
Q8NCK7,SLC16A11,"solute carrier family 16, member 11"
P09417,QDPR,quinoid dihydropteridine reductase
O60669,SLC16A7,"solute carrier family 16 (monocarboxylate transporter), member 7"
Q9NP78,ABCB9,"ATP-binding cassette, sub-family B (MDR/TAP), member 9"
Q96D53,ADCK4,aarF domain containing kinase 4
A4D1E9,GTPBP10,GTP-binding protein 10 (putative)
P26639,TARS,threonyl-tRNA synthetase
P30536,TSPO,translocator protein (18kDa)
P02794,FTH1,"ferritin, heavy polypeptide 1"
Q9NXH9,TRMT1,tRNA methyltransferase 1 homolog (S. cerevisiae)
P60900,PSMA6,"proteasome (prosome, macropain) subunit, alpha type, 6"
Q7Z695,ADCK2,aarF domain containing kinase 2
O15254,ACOX3,"acyl-CoA oxidase 3, pristanoyl"
Q15286,RAB35,"RAB35, member RAS oncogene family"
H0UI37,TSTD3,thiosulfate sulfurtransferase (rhodanese)-like domain containing 3
P82909,MRPS36,mitochondrial ribosomal protein S36
Q9P2J9,PDP2,pyruvate dehyrogenase phosphatase catalytic subunit 2
Q9NUQ2,AGPAT5,1-acylglycerol-3-phosphate O-acyltransferase 5
Q9BUT9,FAM195A,"family with sequence similarity 195, member A"
P55851,UCP2,"uncoupling protein 2 (mitochondrial, proton carrier)"
Q9NYZ2,SLC25A37,"solute carrier family 25 (mitochondrial iron transporter), member 37"
Q96A46,SLC25A28,"solute carrier family 25 (mitochondrial iron transporter), member 28"
Q6ZT89,SLC25A48,"solute carrier family 25, member 48"
Q8WUT9,SLC25A43,"solute carrier family 25, member 43"
Q6Q0C1,SLC25A47,"solute carrier family 25, member 47"
Q8N5S1,SLC25A41,"solute carrier family 25, member 41"
Q6PIV7,SLC25A34,"solute carrier family 25, member 34"
Q9UNF0,PACSIN2,protein kinase C and casein kinase substrate in neurons 2
P21399,ACO1,"aconitase 1, soluble"
P40692,MLH1,mutL homolog 1
P11586,MTHFD1,"methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 1, methenyltetrahydrofolate cyclohydrolase, formyltetrahydrofolate synthetase"
P57772,EEFSEC,"eukaryotic elongation factor, selenocysteine-tRNA-specific"
P34913,EPHX2,"epoxide hydrolase 2, cytoplasmic"
Q15392,DHCR24,24-dehydrocholesterol reductase
Q9UKK9,NUDT5,nudix (nucleoside diphosphate linked moiety X)-type motif 5
Q9BPX6,MICU1,mitochondrial calcium uptake 1
P00441,SOD1,"superoxide dismutase 1, soluble"
Q9H4I8,SERHL2,serine hydrolase-like 2
Q562E7,WDR81,WD repeat domain 81
Q9BU61,NDUFAF3,"NADH dehydrogenase (ubiquinone) complex I, assembly factor 3"
Q53S33,BOLA3,bolA family member 3
Q56VL3,OCIAD2,OCIA domain containing 2
Q9HA92,RSAD1,radical S-adenosyl methionine domain containing 1
Q6PIU2,NCEH1,neutral cholesterol ester hydrolase 1
Q9BRQ6,CHCHD6,coiled-coil-helix-coiled-coil-helix domain containing 6
P60174,TPI1,triosephosphate isomerase 1
Q9NYY8,FASTKD2,FAST kinase domains 2
O96011,PEX11B,peroxisomal biogenesis factor 11 beta
Q96B77,TMEM186,transmembrane protein 186
Q5VST9,OBSCN,"obscurin, cytoskeletal calmodulin and titin-interacting RhoGEF"
P00167,CYB5A,cytochrome b5 type A (microsomal)
Q9H611,PIF1,PIF1 5'-to-3' DNA helicase
P07148,FABP1,"fatty acid binding protein 1, liver"
P33897,ABCD1,"ATP-binding cassette, sub-family D (ALD), member 1"
P04406,GAPDH,glyceraldehyde-3-phosphate dehydrogenase
O94903,PROSC,proline synthetase co-transcribed homolog (bacterial)
Q9UBI4,STOML1,stomatin (EPB72)-like 1
P07108,DBI,"diazepam binding inhibitor (GABA receptor modulator, acyl-CoA binding protein)"
P42356,PI4KA,"phosphatidylinositol 4-kinase, catalytic, alpha"
Q8TCS8,PNPT1,polyribonucleotide nucleotidyltransferase 1
Q9HC24,TMBIM4,transmembrane BAX inhibitor motif containing 4
Q969P6,TOP1MT,"topoisomerase (DNA) I, mitochondrial"
Q8WUR7,C15orf40,chromosome 15 open reading frame 40
O60930,RNASEH1,ribonuclease H1
Q8IUA7,ABCA9,"ATP-binding cassette, sub-family A (ABC1), member 9"
P22307,SCP2,sterol carrier protein 2
Q86UY8,NT5DC3,5'-nucleotidase domain containing 3
P29074,PTPN4,"protein tyrosine phosphatase, non-receptor type 4 (megakaryocyte)"
P56277,CMC4,C-x(9)-C motif containing 4
Q15067,ACOX1,"acyl-CoA oxidase 1, palmitoyl"
P07195,LDHB,lactate dehydrogenase B
P58557,YBEY,ybeY metallopeptidase (putative)
P49773,HINT1,histidine triad nucleotide binding protein 1
P30613,PKLR,"pyruvate kinase, liver and RBC"
Q969V5,MUL1,mitochondrial E3 ubiquitin protein ligase 1
O00142,TK2,"thymidine kinase 2, mitochondrial"
Q9BSE5,AGMAT,agmatine ureohydrolase (agmatinase)
Q5EBM0,CMPK2,"cytidine monophosphate (UMP-CMP) kinase 2, mitochondrial"
P55957,BID,BH3 interacting domain death agonist
P36404,ARL2,ADP-ribosylation factor-like 2
P57105,SYNJ2BP,synaptojanin 2 binding protein
Q9GZY8,MFF,mitochondrial fission factor
Q7Z4W1,DCXR,dicarbonyl/L-xylulose reductase
Q9BW91,NUDT9,nudix (nucleoside diphosphate linked moiety X)-type motif 9
Q9UHK6,AMACR,alpha-methylacyl-CoA racemase
P53370,NUDT6,nudix (nucleoside diphosphate linked moiety X)-type motif 6
Q9NW81,ATP5SL,ATP5S-like
Q9UI43,FTSJ2,FtsJ RNA methyltransferase homolog 2 (E. coli)
Q16611,BAK1,BCL2-antagonist/killer 1
Q02127,DHODH,dihydroorotate dehydrogenase (quinone)
P27338,MAOB,monoamine oxidase B
O14880,MGST3,microsomal glutathione S-transferase 3
Q9NPH0,ACP6,"acid phosphatase 6, lysophosphatidic"
Q96GC5,MRPL48,mitochondrial ribosomal protein L48
P21549,AGXT,alanine-glyoxylate aminotransferase
P00387,CYB5R3,cytochrome b5 reductase 3
Q9NUL7,DDX28,DEAD (Asp-Glu-Ala-Asp) box polypeptide 28
Q12983,BNIP3,BCL2/adenovirus E1B 19kDa interacting protein 3
Q9UIF7,MUTYH,mutY homolog
O43824,GTPBP6,GTP binding protein 6 (putative)
P05108,CYP11A1,"cytochrome P450, family 11, subfamily A, polypeptide 1"
Q9NX40,OCIAD1,OCIA domain containing 1
Q9H825,METTL8,methyltransferase like 8
Q96CM3,RPUSD4,RNA pseudouridylate synthase domain containing 4
O75414,NME6,NME/NM23 nucleoside diphosphate kinase 6
Q14318,FKBP8,"FK506 binding protein 8, 38kDa"
Q86UT6,NLRX1,NLR family member X1
Q96CU9,FOXRED1,FAD-dependent oxidoreductase domain containing 1
Q9H5Q4,TFB2M,"transcription factor B2, mitochondrial"
Q8N3J5,PPM1K,"protein phosphatase, Mg2+/Mn2+ dependent, 1K"
Q06055,ATP5G2,"ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9)"
P03886,ND1,"NADH dehydrogenase, subunit 1 (complex I)"
Q8IXL7,MSRB3,methionine sulfoxide reductase B3
Q9BS92,NIPSNAP3B,nipsnap homolog 3B (C. elegans)
P78549,NTHL1,nth endonuclease III-like 1 (E. coli)
Q9NX47,5-Mar,membrane-associated ring finger (C3HC4) 5
Q6P4A7,SFXN4,sideroflexin 4
P12236,SLC25A6,"solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 6"
O15527,OGG1,8-oxoguanine DNA glycosylase
Q9BXR0,QTRT1,queuine tRNA-ribosyltransferase 1
Q9BRQ8,AIFM2,"apoptosis-inducing factor, mitochondrion-associated, 2"
P32119,PRDX2,peroxiredoxin 2
Q9UKA2,FBXL4,F-box and leucine-rich repeat protein 4
Q9HCL2,GPAM,"glycerol-3-phosphate acyltransferase, mitochondrial"
Q99766,ATP5S,"ATP synthase, H+ transporting, mitochondrial Fo complex, subunit s (factor B)"
Q96TC7,RMDN3,regulator of microtubule dynamics 3
Q9BRX8,FAM213A,"family with sequence similarity 213, member A"
Q96IX5,USMG5,up-regulated during skeletal muscle growth 5 homolog (mouse)
Q6UWS5,PET117,PET117 homolog (S. cerevisiae)
P21397,MAOA,monoamine oxidase A
A6NNL5,C15orf61,chromosome 15 open reading frame 61
P40305,IFI27,"interferon, alpha-inducible protein 27"
Q9Y4U1,MMACHC,"methylmalonic aciduria (cobalamin deficiency) cblC type, with homocystinuria"
P62244,RPS15A,ribosomal protein S15a
Q08257,CRYZ,"crystallin, zeta (quinone reductase)"
P32322,PYCR1,pyrroline-5-carboxylate reductase 1
P13647,KRT5,keratin 5
P62906,RPL10A,ribosomal protein L10a
Q9NVH6,TMLHE,"trimethyllysine hydroxylase, epsilon"
Q15388,TOMM20,translocase of outer mitochondrial membrane 20 homolog (yeast)
P62263,RPS14,ribosomal protein S14
Q96BR5,COA7,cytochrome c oxidase assembly factor 7 (putative)
Q9NQG6,MIEF1,mitochondrial elongation factor 1
Q8NBX0,SCCPDH,saccharopine dehydrogenase (putative)
Q9C002,C15orf48,chromosome 15 open reading frame 48
O60238,BNIP3L,BCL2/adenovirus E1B 19kDa interacting protein 3-like
Q7L8L6,FASTKD5,FAST kinase domains 5
Q99497,PARK7,parkinson protein 7
P54136,RARS,arginyl-tRNA synthetase
O60333,KIF1B,kinesin family member 1B
Q9GZY4,COA1,cytochrome c oxidase assembly factor 1 homolog (S. cerevisiae)
P03901,ND4L,"NADH dehydrogenase, subunit 4L (complex I)"
Q9Y6E7,SIRT4,sirtuin 4
Q9BRT2,UQCC2,ubiquinol-cytochrome c reductase complex assembly factor 2
Q6L8Q7,PDE12,phosphodiesterase 12
Q13232,NME3,NME/NM23 nucleoside diphosphate kinase 3
Q7L2E3,DHX30,DEAH (Asp-Glu-Ala-His) box helicase 30
Q14296,FASTK,Fas-activated serine/threonine kinase
A6NJ78,METTL15,methyltransferase like 15
Q07973,CYP24A1,"cytochrome P450, family 24, subfamily A, polypeptide 1"
Q9BZ23,PANK2,pantothenate kinase 2
P35218,CA5A,"carbonic anhydrase VA, mitochondrial"
Q9H857,NT5DC2,5'-nucleotidase domain containing 2
P14621,ACYP2,"acylphosphatase 2, muscle type"
Q5T9A4,ATAD3B,"ATPase family, AAA domain containing 3B"
O95900,TRUB2,TruB pseudouridine (psi) synthase family member 2
Q86VU5,COMTD1,catechol-O-methyltransferase domain containing 1
Q8TCG5,CPT1C,carnitine palmitoyltransferase 1C
Q6P1S2,C3orf33,chromosome 3 open reading frame 33
Q7KZF4,SND1,staphylococcal nuclease and tudor domain containing 1
Q5VTE6,ANGEL2,angel homolog 2 (Drosophila)
Q13162,PRDX4,peroxiredoxin 4
Q99832,CCT7,"chaperonin containing TCP1, subunit 7 (eta)"
P07237,P4HB,"prolyl 4-hydroxylase, beta polypeptide"
Q9UBZ4,APEX2,APEX nuclease (apurinic/apyrimidinic endonuclease) 2
P22234,PAICS,"phosphoribosylaminoimidazole carboxylase, phosphoribosylaminoimidazole succinocarboxamide synthetase"
Q8TDB4,MGARP,mitochondria-localized glutamic acid-rich protein
Q9BSH5,HDHD3,haloacid dehalogenase-like hydrolase domain containing 3
Q8IV42,PSTK,phosphoseryl-tRNA kinase
P19099,CYP11B2,"cytochrome P450, family 11, subfamily B, polypeptide 2"
P31939,ATIC,5-aminoimidazole-4-carboxamide ribonucleotide formyltransferase/IMP cyclohydrolase
Q96I51,WBSCR16,Williams-Beuren syndrome chromosome region 16
Q8N0U4,FAM185A,"family with sequence similarity 185, member A"
Q13794,PMAIP1,phorbol-12-myristate-13-acetate-induced protein 1
O95881,TXNDC12,thioredoxin domain containing 12 (endoplasmic reticulum)
Q9UG63,ABCF2,"ATP-binding cassette, sub-family F (GCN20), member 2"
Q9Y2W6,TDRKH,tudor and KH domain containing
O15528,CYP27B1,"cytochrome P450, family 27, subfamily B, polypeptide 1"
Q9UHN1,POLG2,"polymerase (DNA directed), gamma 2, accessory subunit"
Q6NXT4,SLC30A6,"solute carrier family 30 (zinc transporter), member 6"
Q9BV47,DUSP26,dual specificity phosphatase 26 (putative)
Q99551,MTERF,mitochondrial transcription termination factor
P36969,GPX4,glutathione peroxidase 4
Q9H015,SLC22A4,"solute carrier family 22 (organic cation/zwitterion transporter), member 4"
P21964,COMT,catechol-O-methyltransferase
Q86UA3,C12orf10,chromosome 12 open reading frame 10
Q8TB22,SPATA20,spermatogenesis associated 20
P63218,GNG5,"guanine nucleotide binding protein (G protein), gamma 5"
Q96BQ5,CCDC127,coiled-coil domain containing 127
Q16526,CRY1,cryptochrome circadian clock 1
O60488,ACSL4,acyl-CoA synthetase long-chain family member 4
Q9BQP7,MGME1,mitochondrial genome maintenance exonuclease 1
O43236,4-Sep,septin 4
Q15006,EMC2,ER membrane protein complex subunit 2
Q9BUP0,EFHD1,"EF-hand domain family, member D1"
Q9BUV8,C20orf24,chromosome 20 open reading frame 24
O15270,SPTLC2,"serine palmitoyltransferase, long chain base subunit 2"
O95994,AGR2,anterior gradient 2
Q8TCD5,NT5C,"5', 3'-nucleotidase, cytosolic"
Q13772,NCOA4,nuclear receptor coactivator 4
Q8WWR8,NEU4,sialidase 4
Q53H12,AGK,acylglycerol kinase
Q9NX74,DUS2,dihydrouridine synthase 2
Q15785,TOMM34,translocase of outer mitochondrial membrane 34
O15091,KIAA0391,KIAA0391
Q9BT92,TCHP,"trichoplein, keratin filament binding"
|UMTCK,CKMT1B,"creatine kinase, mitochondrial 1B"
O75438,NDUFB1,"NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa"
B4DJ38,ATP5J2-PTCD1,ATP5J2-PTCD1 readthrough
Q14790,CASP8,"caspase 8, apoptosis-related cysteine peptidase"
Q07817,BCL2L1,BCL2-like 1
P18077,RPL35A,ribosomal protein L35a
Q8N2F6,ARMC10,armadillo repeat containing 10
P30307,CDC25C,cell division cycle 25C
Q13637,RAB32,"RAB32, member RAS oncogene family"
Q6BCY4,CYB5R2,cytochrome b5 reductase 2
Q9BXF6,RAB11FIP5,RAB11 family interacting protein 5 (class I)
Q9NWX6,THG1L,tRNA-histidine guanylyltransferase 1-like (S. cerevisiae)
Q9H4A6,GOLPH3,golgi phosphoprotein 3 (coat-protein)
Q4J6C6,PREPL,prolyl endopeptidase-like
Q14CZ7,FASTKD3,FAST kinase domains 3
Q96ST8,CEP89,centrosomal protein 89kDa
P80303,NUCB2,nucleobindin 2
Q13488,TCIRG1,"T-cell, immune regulator 1, ATPase, H+ transporting, lysosomal V0 subunit A3"
Q14596,NBR1,neighbor of BRCA1 gene 1
Q14257,RCN2,"reticulocalbin 2, EF-hand calcium binding domain"
Q96AY3,FKBP10,"FK506 binding protein 10, 65 kDa"
Q8NE22,SETD9,SET domain containing 9
P49247,RPIA,ribose 5-phosphate isomerase A
P11047,LAMC1,"laminin, gamma 1 (formerly LAMB2)"
Q92934,BAD,BCL2-associated agonist of cell death
P10415,BCL2,B-cell CLL/lymphoma 2
Q92843,BCL2L2,BCL2-like 2
Q09013,DMPK,dystrophia myotonica-protein kinase
P51530,DNA2,DNA replication helicase/nuclease 2
P03923,ND6,"NADH dehydrogenase, subunit 6 (complex I)"
Q13686,ALKBH1,"alkB, alkylation repair homolog 1 (E. coli)"
Q9NRD5,PICK1,protein interacting with PRKCA 1
O43572,AKAP10,A kinase (PRKA) anchor protein 10
Q9P286,PAK7,p21 protein (Cdc42/Rac)-activated kinase 7
Q9H649,NSUN3,"NOP2/Sun domain family, member 3"
Q96DU9,PABPC5,"poly(A) binding protein, cytoplasmic 5"
Q8N3Z0,PRSS35,"protease, serine, 35"
Q9P241,ATP10D,"ATPase, class V, type 10D"
Q96JX3,SERAC1,serine active site containing 1
P56962,STX17,syntaxin 17
Q9BVS5,TRMT61B,tRNA methyltransferase 61 homolog B (S. cerevisiae)
Q9HBL7,PLGRKT,"plasminogen receptor, C-terminal lysine transmembrane protein"
P49207,RPL34,ribosomal protein L34
Q96T21,SECISBP2,SECIS binding protein 2
P56278,MTCP1,mature T-cell proliferation 1
Q9NTK1,C10orf10,chromosome 10 open reading frame 10
Q8N8R5,C2orf69,chromosome 2 open reading frame 69
Q9NR71,ASAH2,N-acylsphingosine amidohydrolase (non-lysosomal ceramidase) 2
Q9Y696,CLIC4,chloride intracellular channel 4
O95721,SNAP29,"synaptosomal-associated protein, 29kDa"
Q7Z4G4,TRMT11,tRNA methyltransferase 11 homolog (S. cerevisiae)
P0C7Q2,ARMS2,age-related maculopathy susceptibility 2