Uniprot Accession,Protein Names,Gene Names
Q6P4F2,"Adrenodoxin-like protein, mitochondrial;Ferredoxin-1-like protein",FDX1L
Q99757,"Thioredoxin, mitochondrial;Thioredoxin-2",TRX2;TXN2
A4D1V4,"cDNA, FLJ93927, Homo sapiens mitochondrial ribosomal protein L32 (MRPL32), nucleargene encoding mitochondrial protein, mRNA;Mitochondrial ribosomal protein L32;Mitochondrial ribosomal protein L32, isoform CRA_d;39S ribosomal protein L32, mitochondrial",hCG_19886;MRPL32;tcag7.484;HSPC283
P23434,"Glycine cleavage system H protein, mitochondrial",GCSH
Q9NQ50,"39S ribosomal protein L40, mitochondrial;Nuclear localization signal-containing protein deleted in velocardiofacial syndrome;Up-regulated in metastasis",MRPL40;NLVCF;URIM
Q9NZE8,"39S ribosomal protein L35, mitochondrial;Putative uncharacterized protein MRPL35",BM-007;MRPL35
Q4U2R6,"39S ribosomal protein L51, mitochondrial;bMRP-64",CDA09;HSPC241;MRP64;MRPL51
Q9HD34,LYR motif-containing protein 4;Putative uncharacterized protein LYRM4,C6orf149;CGI-203;ISD11;LYRM4
Q96A26,E2-induced gene 5 protein;Protein FAM162A,C3orf28;DC16;E2IG5;FAM162A;FWP001
Q9BQC6,"Ribosomal protein 63, mitochondrial",MRP63
P10109,"Adrenal ferredoxin;Adrenodoxin, mitochondrial;Ferredoxin-1;Hepatoredoxin",ADX;FDX1
Q9NUJ1,"Abhydrolase domain-containing protein 10, mitochondrial;cDNA FLJ50858, highly similar to Homo sapiens abhydrolase domain containing 10 (ABHD10), mRNA",ABHD10
Q8N8R5,UPF0565 protein C2orf69,C2orf69
Q9HAV7,"GrpE protein homolog 1, mitochondrial;HMGE;Mt-GrpE#1;GrpE protein homolog",GREPEL1;GRPEL1
Q9GZT6,"Coiled-coil domain-containing protein 90B, mitochondrial;cDNA FLJ31410 fis, clone NT2NE2000195, highly similar to Homo sapiens MDS025 mRNA;Putative uncharacterized protein MDS025",CCDC90B;CUA003;MDS011;MDS025;hCG_27349
P14927,"Complex III subunit 7;Complex III subunit VII;Cytochrome b-c1 complex subunit 7;QP-C;Ubiquinol-cytochrome c reductase complex 14 kDa protein;cDNA FLJ52271, moderately similar to Ubiquinol-cytochrome c reductase complex 14 kDa protein (EC 1.10.2.2)",UQBP;UQCRB
Q6PI78,Transmembrane protein 65,TMEM65
Q9H2W6,"39S ribosomal protein L46, mitochondrial;P2ECSL",C15orf4;LIECG2;MRPL46
Q9BYC9,"39S ribosomal protein L20, mitochondrial",MRPL20
Q9BYD6,"39S ribosomal protein L1, mitochondrial",BM-022;MRPL1
Q6P587,Fumarylacetoacetate hydrolase domain-containing protein 1;YisK-like protein;Fumarylacetoacetate hydrolase domain containing 1,C16orf36;FAHD1;YISKL;AC012180.10-003
Q13084,"39S ribosomal protein L28, mitochondrial;Melanoma antigen p15;Melanoma-associated antigen recognized by T lymphocytes;Mitochondrial ribosomal protein L28",MAAT1;MRPL28;Z97634.1-001;Z97634.1-010;Z97634.1-009;Z97634.1-011
Q86SX6,"Glutaredoxin-related protein 5, mitochondrial;Monothiol glutaredoxin-5",C14orf87;GLRX5
Q9BPW8,Protein NipSnap homolog 1,NIPSNAP1
P09669,Cytochrome c oxidase polypeptide VIc;Cytochrome c oxidase subunit 6C,COX6C
Q8TCC3,"39S ribosomal protein L28, mitochondrial;39S ribosomal protein L30, mitochondrial;Putative uncharacterized protein MRPL30",HSPC249;MRPL28;MRPL30;RPML28
Q9NNW7,"Selenoprotein Z;Thioredoxin reductase 2, mitochondrial;Thioredoxin reductase TR3;TR-beta;Putative uncharacterized protein TXNRD2",KIAA1652;TRXR2;TXNRD2
Q9BYD2,"39S ribosomal protein L9, mitochondrial;Mitochondrial ribosomal protein L9",MRPL9;RP11-98D18.5-002
Q9Y2R9,"28S ribosomal protein S7, mitochondrial;bMRP-27a",MRPS7
P11182,"Branched-chain alpha-keto acid dehydrogenase complex component E2;Dihydrolipoamide acetyltransferase component of branched-chain alpha-keto acid dehydrogenase complex;Dihydrolipoamide branched chain transacylase;Dihydrolipoyllysine-residue (2-methylpropanoyl)transferase;Lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial;Dihydrolipoamide branched chain transacylase E2",BCATE2;DBT;RP11-305E17.3-002
Q8TCS8,"3-5 RNA exonuclease OLD35;PNPase old-35;Polynucleotide phosphorylase 1;Polynucleotide phosphorylase-like protein;Polyribonucleotide nucleotidyltransferase 1, mitochondrial",PNPASE;PNPT1
P42126,"3,2-trans-enoyl-CoA isomerase, mitochondrial;Delta(3),Delta(2)-enoyl-CoA isomerase;Dodecenoyl-CoA isomerase",DCI
Q13405,"39S ribosomal protein L49, mitochondrial;Neighbor of FAU;Protein NOF1",C11orf4;MRPL49;NOF1;OK/SW-cl.67
Q9P032,Hormone-regulated proliferation-associated protein of 20 kDa;NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 4,C6orf66;HRPAP20;HSPC125;My013;NDUFAF4
O75208,"Ubiquinone biosynthesis protein COQ9, mitochondrial",C16orf49;COQ9;HSPC326;PSEC0129
Q9BQ48,"39S ribosomal protein L34, mitochondrial",MRPL34
Q9BVS5,Potential tRNA (adenine-N(1)-)-methyltransferase catalytic subunit TRMT61B,TRMT61B
Q9UMS0,"HIRA-interacting protein 5;NFU1 iron-sulfur cluster scaffold homolog, mitochondrial;Putative uncharacterized protein NFU1",CGI-33;HIRIP5;NFU1
Q8IXM3,"39S ribosomal protein L27 homolog;39S ribosomal protein L41, mitochondrial;Bcl-2-interacting mitochondrial ribosomal protein L41;Cell proliferation-inducing gene 3 protein;MRP-L27 homolog",BMRP;MRPL27;MRPL41;PIG3;RPML27
Q9BYD3,"39S ribosomal protein L4, mitochondrial",CDABP0091;CGI-28;MRPL4
Q9NZJ6,"3,4-dihydroxy-5-hexaprenylbenzoate methyltransferase;Dihydroxyhexaprenylbenzoate methyltransferase;Hexaprenyldihydroxybenzoate methyltransferase, mitochondrial",COQ3;UG0215E05
P22033,"Methylmalonyl-CoA isomerase;Methylmalonyl-CoA mutase, mitochondrial",MUT
P13073,"Cytochrome c oxidase polypeptide IV;Cytochrome c oxidase subunit 4 isoform 1, mitochondrial;Cytochrome c oxidase subunit IV isoform 1",COX4;COX4I1
P26440,"Isovaleryl-CoA dehydrogenase, mitochondrial;cDNA FLJ16602 fis, clone TESTI4007816, highly similar to Isovaleryl-CoA dehydrogenase, mitochondrial (EC 1.3.99.10);Isovaleryl Coenzyme A dehydrogenase, isoform CRA_b",IVD;hCG_38955
Q16854,"Deoxyguanosine kinase, mitochondrial;Putative uncharacterized protein DGUOK",DGK;DGUOK
P00505,"Aspartate aminotransferase, mitochondrial;Fatty acid-binding protein;Glutamate oxaloacetate transaminase 2;Plasma membrane-associated fatty acid-binding protein;Transaminase A",GOT2
P13196,"5-aminolevulinate synthase, nonspecific, mitochondrial;5-aminolevulinic acid synthase 1;Delta-ALA synthase 1;Delta-aminolevulinate synthase 1;cDNA FLJ53856, highly similar to 5-aminolevulinate synthase, nonspecific, mitochondrial (EC 2.3.1.37)",ALAS1;ALAS3;ALASH;OK/SW-cl.121
Q9UGM6,"(Mt)TrpRS;Tryptophan--tRNA ligase;Tryptophanyl-tRNA synthetase, mitochondrial;cDNA FLJ50844, highly similar to Tryptophanyl-tRNA synthetase, mitochondrial (EC 6.1.1.2)",WARS2
P23368,"Malic enzyme 2;NAD-dependent malic enzyme, mitochondrial;Malic enzyme",ME2;hCG_23687
O95202,"LETM1 and EF-hand domain-containing protein 1, mitochondrial;Leucine zipper-EF-hand-containing transmembrane protein 1",LETM1
Q5U5X0,LYR motif-containing protein 7,C5orf31;LYRM7
P30048,"Antioxidant protein 1;HBC189;Peroxiredoxin III;Peroxiredoxin-3;Protein MER5 homolog;Thioredoxin-dependent peroxide reductase, mitochondrial",AOP1;PRDX3
Q00059,"Mitochondrial transcription factor 1;Transcription factor 6;Transcription factor 6-like 2;Transcription factor A, mitochondrial;Putative uncharacterized protein TFAM",TCF6;TCF6L2;TFAM
Q9H9J2,"39S ribosomal protein L44, mitochondrial",MRPL44
Q96HY7,"Dehydrogenase E1 and transketolase domain-containing protein 1;Probable 2-oxoglutarate dehydrogenase E1 component DHKTD1, mitochondrial",DHTKD1;KIAA1630
P38117,Electron transfer flavoprotein subunit beta,ETFB;FP585
Q96A35,"39S ribosomal protein L24, mitochondrial",MRPL24
P10606,"Cytochrome c oxidase polypeptide Vb;Cytochrome c oxidase subunit 5B, mitochondrial",COX5B
Q13825,"AU-specific RNA-binding enoyl-CoA hydratase;Methylglutaconyl-CoA hydratase, mitochondrial",AUH
P27144,"Adenylate kinase 3-like;Adenylate kinase isoenzyme 4, mitochondrial;ATP-AMP transphosphorylase;HCG2031840, isoform CRA_c",AK3;AK3L1;AK3L2;AK4;hCG_2031840
Q10713,"Alpha-MPP;Mitochondrial-processing peptidase subunit alpha;P-55;cDNA FLJ54999, highly similar to Mitochondrial-processing peptidase alpha subunit, mitochondrial (EC 3.4.24.64)",INPP5E;KIAA0123;MPPA;PMPCA
Q12849,"G-rich sequence factor 1;cDNA FLJ30937 fis, clone FEBRA2007247, highly similar to G-rich sequence factor 1;cDNA FLJ32329 fis, clone PROST2004526, highly similar to G-rich sequence factor 1;cDNA FLJ37487 fis, clone BRAWH2014511, highly similar to G-rich sequence factor 1;cDNA FLJ38480 fis, clone FEBRA2022911, highly similar to G-rich sequence factor 1;cDNA FLJ39736 fis, clone SMINT2016313, highly similar to G-rich sequence factor 1;G-rich RNA sequence binding factor 1, isoform CRA_a",GRSF1;hCG_17000
Q9H2U2,"Inorganic pyrophosphatase 2, mitochondrial;Pyrophosphatase SID6-306;Pyrophosphate phospho-hydrolase 2",HSPC124;PPA2
Q9Y276,BCS1-like protein;Mitochondrial chaperone BCS1,BCS1;BCS1L
Q7Z2W9,"39S ribosomal protein L21, mitochondrial;cDNA FLJ52689, highly similar to Homo sapiens mitochondrial ribosomal protein L21 (MRPL21), transcript variant 4, mRNA;Mitochondrial ribosomal protein L21, isoform CRA_a;Putative uncharacterized protein MRPL21",MRPL21;hCG_27184
Q8N5N7,"39S ribosomal protein L50, mitochondrial;cDNA FLJ52265, highly similar to Homo sapiens mitochondrial ribosomal protein L50 (MRPL50), mRNA",MRPL50
P56181,"NADH dehydrogenase [ubiquinone] flavoprotein 3, isoform 2",NDUFV3
Q96GC5,"39S ribosomal protein L48, mitochondrial;cDNA FLJ60720, highly similar to Homo sapiens mitochondrial ribosomal protein L48 (MRPL48), transcript variant 1, mRNA",CGI-118;HSPC290;MRPL48
Q5T653,"39S ribosomal protein L2, mitochondrial",CGI-22;MRPL2
Q8N183,"B17.2-like;Mimitin, mitochondrial;Myc-induced mitochondrial protein;NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 2;NDUFA12-like protein",NDUFA12L;NDUFAF2
Q8IYB8,"ATP-dependent RNA helicase SUPV3L1, mitochondrial;Suppressor of var1 3-like protein 1",SUPV3L1;SUV3
Q9P015,"39S ribosomal protein L15, mitochondrial",HSPC145;MRPL15
Q9Y3D7,Mitochondria-associated granulocyte macrophage CSF-signaling molecule;Mitochondrial import inner membrane translocase subunit Tim16,CGI-136;MAGMAS;TIM16;TIMM16
Q5T1C6,Carboxyl-terminal modulator protein;Thioesterase superfamily member 4,CTMP;THEM4
P53370,Antisense basic fibroblast growth factor;Nucleoside diphosphate-linked moiety X motif 6;Protein GFG,FGF2AS;NUDT6
O43766,"Lipoate synthase;Lipoic acid synthase;Lipoyl synthase, mitochondrial;Putative uncharacterized protein LIAS",HUSSY-01;LAS;LIAS
Q9GZT3,"SRA stem-loop-interacting RNA-binding protein, mitochondrial",C14orf156;DC23;DC50;PD04872;SLIRP
Q9HD33,"39S ribosomal protein L47, mitochondrial;Nasopharyngeal carcinoma metastasis-related protein 1",CGI-204;MRPL47;NCM1
O75323,"Glioblastoma-amplified sequence;Protein NipSnap homolog 2;Glioblastoma amplified sequence, isoform CRA_a;Putative uncharacterized protein GBAS",GBAS;NIPSNAP2;hCG_18231
Q8TAE8,CKII beta-associating protein;CR6-interacting factor 1;Growth arrest and DNA damage-inducible proteins-interacting protein 1;p53-responsive gene 6 protein;Papillomavirus L2-interacting nuclear protein 1,GADD45GIP1;PLINP1;PRG6
Q96EY8,"Cob(I)alamin adenosyltransferase;Cob(I)yrinic acid a,c-diamide adenosyltransferase, mitochondrial;Methylmalonic aciduria type B protein",MMAB
Q86TS9,"39S ribosomal protein L52, mitochondrial;Mitochondrial ribosomal protein L52, isoform CRA_c;Putative uncharacterized protein MRPL52",MRPL52;hCG_41985
O75390,"Citrate synthase, mitochondrial;Citrate synthase",CS
O14548,"COX7a-related protein;Cytochrome c oxidase subunit 7A-related protein, mitochondrial;Cytochrome c oxidase subunit VIIa-related protein;EB1",COX7A2L;COX7AR;COX7RP
Q5TEU4,"Probable methyltransferase C20orf7, mitochondrial;cDNA FLJ33741 fis, clone BRAWH2018875, weakly similar to Protein At1g22800;HCG1811060, isoform CRA_c",C20orf7;hCG_1811060
Q9NU23,LYR motif-containing protein 2,LYRM2
P78540,"Arginase-2, mitochondrial;Kidney-type arginase;Non-hepatic arginase;Type II arginase",ARG2
Q9NRX2,"39S ribosomal protein L17, mitochondrial;LYST-interacting protein 2",LIP2;MRPL17
Q9H0U6,"39S ribosomal protein L18, mitochondrial",HSPC071;MRPL18
Q9BX68,"HINT-3;Histidine triad nucleotide-binding protein 2, mitochondrial;HIT-17kDa;PKCI-1-related HIT protein",HINT2
Q8NCN5,"Pyruvate dehydrogenase phosphatase regulatory subunit, mitochondrial;Putative uncharacterized protein ENSP00000381190",KIAA1990;PDPR
Q9UFN0,Protein NipSnap homolog 3A;Protein NipSnap homolog 4;Target for Salmonella secreted protein C,HSPC299;NIPSNAP3A;NIPSNAP4
P36957,"2-oxoglutarate dehydrogenase complex component E2;Dihydrolipoamide succinyltransferase component of 2-oxoglutarate dehydrogenase complex;Dihydrolipoyllysine-residue succinyltransferase component of 2-oxoglutarate dehydrogenase complex, mitochondrial;E2K;cDNA FLJ55034, highly similar to Dihydrolipoyllysine-residue succinyltransferase component of 2- oxoglutarate dehydrogenase complex, mitochondrial (EC 2.3.1.61);Full-length cDNA 5-PRIME end of clone CS0DJ009YL13 of T cells (Jurkat cell line) of Homo sapiens (human)",DLST;DLTS
P51398,"28S ribosomal protein S29, mitochondrial;Death-associated protein 3;Ionizing radiation resistance conferring protein;cDNA FLJ57409, highly similar to Mitochondrial 28S ribosomal protein S29;Death associated protein 3, isoform CRA_d",DAP3;MRPS29;hCG_17177
Q9NP92,"28S ribosomal protein S30, mitochondrial;Programmed cell death protein 9",BM-047;MRPS30;PDCD9
O14561,"Acyl carrier protein, mitochondrial;CI-SDAP;NADH-ubiquinone oxidoreductase 9.6 kDa subunit",NDUFAB1
P82673,"28S ribosomal protein S28, mitochondrial;28S ribosomal protein S35, mitochondrial",HDCMD11P;MDS023;MRPS28;MRPS35;PSEC0213
Q9UHN1,"DNA polymerase gamma accessory 55 kDa subunit;DNA polymerase subunit gamma-2, mitochondrial;Mitochondrial DNA polymerase accessory subunit;MtPolB;PolG-beta",MTPOLB;POLG2
O43676,Complex I-B12;NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 3;NADH-ubiquinone oxidoreductase B12 subunit;Putative uncharacterized protein NDUFB3,NDUFB3
Q96DV4,"39S ribosomal protein L38, mitochondrial;cDNA FLJ13996 fis, clone Y79AA1002211, highly similar to Homo sapiens mitochondrial ribosomal protein L38 (MRPL38), nuclear gene encoding mitochondrial protein, mRNA",HSPC262;MRPL38
P42704,"130 kDa leucine-rich protein;GP130;Leucine-rich PPR motif-containing protein, mitochondrial",LRP130;LRPPRC
Q96EY7,"Pentatricopeptide repeat-containing protein 3, mitochondrial;Transformation-related gene 15 protein",PTCD3;TRG15
Q14197,"Digestion substraction 1;Immature colon carcinoma transcript 1 protein;Peptidyl-tRNA hydrolase ICT1, mitochondrial",DS1;ICT1
E7ETU7,"39S ribosomal protein L3, mitochondrial",MRL3;MRPL3;RPML3
P10515,"70 kDa mitochondrial autoantigen of primary biliary cirrhosis;Dihydrolipoamide acetyltransferase component of pyruvate dehydrogenase complex;Dihydrolipoyllysine-residue acetyltransferase component of pyruvate dehydrogenase complex, mitochondrial;M2 antigen complex 70 kDa subunit;Pyruvate dehydrogenase complex component E2",DLAT;DLTA
P82664,"28S ribosomal protein S10, mitochondrial",MRPS10;MSTP040
O75489,"Complex I-30kD;NADH dehydrogenase [ubiquinone] iron-sulfur protein 3, mitochondrial;NADH-ubiquinone oxidoreductase 30 kDa subunit",NDUFS3
Q6YP21,"Cysteine-S-conjugate beta-lyase 2;Kynurenine aminotransferase III;Kynurenine--glyoxylate transaminase;Kynurenine--oxoglutarate transaminase 3;Kynurenine--oxoglutarate transaminase III;cDNA FLJ32614 fis, clone STOMA2000121, highly similar to Homo sapiens kynurenine aminotransferase III (KAT3), transcript variant 2, mRNA",CCBL2;KAT3;RBMXL1
Q5T4U5,"Acyl-Coenzyme A dehydrogenase, C-4 to C-12 straight chain;Acyl-Coenzyme A dehydrogenase, C-4 to C-12 straight chain, isoform CRA_a;Medium-chain specific acyl-CoA dehydrogenase, mitochondrial;cDNA, FLJ78845, highly similar to Medium-chain specific acyl-CoA dehydrogenase, mitochondrial (EC 1.3.99.3);cDNA FLJ52595, highly similar to Medium-chain specific acyl-CoA dehydrogenase, mitochondrial (EC 1.3.99.3)",ACADM;hCG_22915;RP4-682C21.1-002
Q92665,"28S ribosomal protein S31, mitochondrial;Imogen 38",IMOGN38;MRPS31
G3V1M7,"Very long-chain specific acyl-CoA dehydrogenase, mitochondrial",ACADVL;VLCAD
Q9BYD1,"39S ribosomal protein L13, mitochondrial",MRPL13
Q9P0M9,"39S ribosomal protein L27, mitochondrial",HSPC250;MRPL27
Q4G0N4,UPF0465 protein C5orf33;cDNA FLJ55867,C5orf33
Q8WW59,"SPRY domain-containing protein 4;cDNA FLJ53756, highly similar to SPRY domain-containing protein 4",SPRYD4
O15382,"Branched-chain-amino-acid aminotransferase, mitochondrial;Placental protein 18;Branched-chain-amino-acid aminotransferase",BCAT2;BCATM;BCT2;ECA40
Q96E29,"mTERF domain-containing protein 1, mitochondrial",CGI-12;MTERFD1
Q9H1K1,"Iron-sulfur cluster assembly enzyme ISCU, mitochondrial;NifU-like N-terminal domain-containing protein;NifU-like protein;cDNA FLJ32689 fis, clone TESTI2000207, highly similar to NifU-like N-terminal domain-containing protein, mitochondrial;cDNA FLJ51257, highly similar to NifU-like N-terminal domain-containing protein, mitochondrial;ICSU;ISCU",ISCU;NIFUN
Q8IWL3,"DnaJ homolog subfamily C member 20;Hsc20;Iron-sulfur cluster co-chaperone protein HscB, mitochondrial;HscB iron-sulfur cluster co-chaperone homolog (E. coli);J-type co-chaperone HSC20, isoform CRA_c;Putative uncharacterized protein HSCB",DNAJC20;HSC20;HSCB;hCG_40981;RP3-366L4.2;RP3-366L4.3-003
P38646,"75 kDa glucose-regulated protein;Heat shock 70 kDa protein 9;Mortalin;Peptide-binding protein 74;Stress-70 protein, mitochondrial;cDNA FLJ51907, highly similar to Stress-70 protein, mitochondrial",GRP75;HSPA9;HSPA9B
Q16836,"Hydroxyacyl-coenzyme A dehydrogenase, mitochondrial;Medium and short-chain L-3-hydroxyacyl-coenzyme A dehydrogenase;Short-chain 3-hydroxyacyl-CoA dehydrogenase",HAD;HADH;HADHSC;SCHAD
Q16718,Complex I subunit B13;Complex I-13kD-B;NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 5;NADH-ubiquinone oxidoreductase 13 kDa-B subunit;Putative uncharacterized protein DKFZp781K1356;Putative uncharacterized protein NDUFA5,NDUFA5;DKFZp781K1356
A4D154,"cDNA FLJ45842 fis, clone NTONG2009468;cDNA, FLJ92099;Chromosome 7 open reading frame 30;Uncharacterized protein C7orf30",C7orf30;hCG_37983;tcag7.1243
O43678,Complex I-B8;NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 2;NADH-ubiquinone oxidoreductase B8 subunit,NDUFA2
P21912,"Iron-sulfur subunit of complex II;Succinate dehydrogenase [ubiquinone] iron-sulfur subunit, mitochondrial",SDH;SDH1;SDHB
O95139,"Complex I-B17;NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 6;NADH-ubiquinone oxidoreductase B17 subunit;NADH dehydrogenase (Ubiquinone) 1 beta subcomplex, 6, 17kDa;NADH dehydrogenase (Ubiquinone) 1 beta subcomplex, 6, 17kDa, isoform CRA_b",NDUFB6;hCG_30272;RP11-205M20.6-002
P49406,"39S ribosomal protein L15, mitochondrial;39S ribosomal protein L19, mitochondrial",KIAA0104;MRPL15;MRPL19
Q16540,"39S ribosomal protein L23, mitochondrial;L23 mitochondrial-related protein;Ribosomal protein L23-like;Putative uncharacterized protein MRPL23",L23MRP;MRPL23;RPL23L
Q9NX14,"Complex I-ESSS;NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 11, mitochondrial;NADH-ubiquinone oxidoreductase ESSS subunit;Neuronal protein 17.3",NDUFB11;UNQ111/PRO1064
Q9UII2,"ATPase inhibitor, mitochondrial;Inhibitor of F(1)F(o)-ATPase",ATPI;ATPIF1
P05091,"Aldehyde dehydrogenase, mitochondrial;ALDH class 2;ALDH-E2;ALDHI",ALDH2;ALDM
Q96EL2,"28S ribosomal protein S24, mitochondrial;bMRP-47;Putative uncharacterized protein MRPS24",HSPC335;MRPS24
Q9NWU1,"3-oxoacyl-[acyl-carrier-protein] synthase, mitochondrial;Beta-ketoacyl-ACP synthase;Putative uncharacterized protein OXSM",OXSM
O75947,"ATP synthase subunit d, mitochondrial",ATP5H;My032
Q7Z7F7,"39S ribosomal protein L55, mitochondrial",MRPL55;UNQ5835/PRO19675
Q96DA6,"DnaJ homolog subfamily C member 19;Mitochondrial import inner membrane translocase subunit TIM14;DnaJ (Hsp40) homolog, subfamily C, member 19, isoform CRA_a;Putative uncharacterized protein DNAJC19",DNAJC19;TIM14;TIMM14;hCG_17532
P34897,"Glycine hydroxymethyltransferase;Serine hydroxymethyltransferase, mitochondrial;Serine methylase;Serine hydroxymethyltransferase;cDNA FLJ58585, highly similar to Serine hydroxymethyltransferase, mitochondrial (EC 2.1.2.1);Serine hydroxymethyltransferase 2 (Mitochondrial), isoform CRA_h",SHMT2;hCG_41231
A4D1U3,"cDNA, FLJ93504, Homo sapiens single-stranded DNA binding protein 1 (SSBP1), mRNA;Single-stranded DNA binding protein 1;Single-stranded DNA binding protein 1, isoform CRA_a;PWP1-interacting protein 17;Single-stranded DNA-binding protein, mitochondrial;Putative uncharacterized protein SSBP1",hCG_2014251;SSBP1;tcag7.401;SSBP
P31937,"3-hydroxyisobutyrate dehydrogenase, mitochondrial;3-hydroxyisobutyrate dehydrogenase;3-hydroxyisobutyrate dehydrogenase;3-hydroxyisobutyrate dehydrogenase, isoform CRA_a;cDNA, FLJ96784, Homo sapiens 3-hydroxyisobutyrate dehydrogenase (HIBADH), mRNA;NS5ATP1",HIBADH;hCG_39034;NS5ATP1;tcag7.211
Q16595,"Frataxin intermediate form;Frataxin(56-210);Frataxin(81-210);Frataxin, mitochondrial;Friedreich ataxia protein;Putative uncharacterized protein FXN",FRDA;FXN;X25
Q5T440,"Putative transferase C1orf69, mitochondrial",C1orf69
Q9Y3B8,"Oligoribonuclease, mitochondrial;RNA exonuclease 2 homolog;Small fragment nuclease",CGI-114;REXO2;SFN;SMFN
P30405,"Cyclophilin F;Peptidyl-prolyl cis-trans isomerase F, mitochondrial;Rotamase F;Peptidyl-prolyl cis-trans isomerase",CYP3;PPIF;hCG_22611
Q9BSH5,Haloacid dehalogenase-like hydrolase domain-containing protein 3,C9orf158;HDHD3
P30042,"ES1 protein homolog, mitochondrial;Protein GT335;Protein KNP-I",C21orf33;HES1;KNPI
P23378,"Glycine cleavage system P protein;Glycine decarboxylase;Glycine dehydrogenase [decarboxylating], mitochondrial",GCSP;GLDC
Q9NVH6,"Epsilon-trimethyllysine 2-oxoglutarate dioxygenase;Epsilon-trimethyllysine hydroxylase;TML hydroxylase;TML-alpha-ketoglutarate dioxygenase;Trimethyllysine dioxygenase, mitochondrial",TMLH;TMLHE
O75380,"Complex I-13kD-A;NADH dehydrogenase [ubiquinone] iron-sulfur protein 6, mitochondrial;NADH-ubiquinone oxidoreductase 13 kDa-A subunit",NDUFS6
Q9BZE1,"39S ribosomal protein L2, mitochondrial;39S ribosomal protein L37, mitochondrial",HSPC235;MRPL2;MRPL37;RPML2
Q9HD23,"Magnesium transporter MRS2 homolog, mitochondrial;MRS2-like protein;cDNA FLJ52725, highly similar to Magnesium transporter MRS2L, mitochondrial",HPT;MRS2;MRS2L
Q9NP80,"Calcium-independent phospholipase A2-gamma;Intracellular membrane-associated calcium-independent phospholipase A2 gamma;iPLA2-2;Patatin-like phospholipase domain-containing protein 8;PNPLA-gamma;Intracellular membrane-associated calcium-independent phospholipase A2 gamma, isoform CRA_b;Putative uncharacterized protein PNPLA8",BM-043;IPLA22;IPLA2G;PNPLA8;hCG_17116;IPLA2(GAMMA)
P35914,"3-hydroxy-3-methylglutarate-CoA lyase;Hydroxymethylglutaryl-CoA lyase, mitochondrial;3-hydroxymethyl-3-methylglutaryl-Coenzyme A lyase;3-hydroxymethyl-3-methylglutaryl-Coenzyme A lyase (Hydroxymethylglutaricaciduria), isoform CRA_b;cDNA FLJ16378 fis, clone TKIDN2016399, highly similar to Hydroxymethylglutaryl-CoA lyase, mitochondrial (EC 4.1.3.4);cDNA FLJ53101, highly similar to Hydroxymethylglutaryl-CoA lyase, mitochondrial (EC 4.1.3.4)",HMGCL;hCG_37683;RP5-886K2.8-001
Q9Y6M9,Complex I-B22;LYR motif-containing protein 3;NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 9;NADH-ubiquinone oxidoreductase B22 subunit,LYRM3;NDUFB9;UQOR22
O75414,Inhibitor of p53-induced apoptosis-alpha;nm23-H6;Nucleoside diphosphate kinase 6;Nucleoside diphosphate kinase,NME6
A2A274,"Aconitase 2, mitochondrial;Aconitate hydratase, mitochondrial;Citrate hydro-lyase;cDNA FLJ50886, highly similar to Aconitate hydratase, mitochondrial(EC 4.2.1.3);cDNA FLJ60429, highly similar to Aconitate hydratase, mitochondrial (EC 4.2.1.3)",ACO2;RP3-347H13.8-002
P40926,"Malate dehydrogenase, mitochondrial",MDH2
O95182,Complex I-B14.5a;NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 7;NADH-ubiquinone oxidoreductase subunit B14.5a,NDUFA7
Q96AB3,"Isochorismatase domain-containing protein 2, mitochondrial",ISOC2
O00330,"Dihydrolipoamide dehydrogenase-binding protein of pyruvate dehydrogenase complex;E3-binding protein;Lipoyl-containing pyruvate dehydrogenase complex component X;proX;Pyruvate dehydrogenase protein X component, mitochondrial",PDHX;PDX1
Q9UI09,13 kDa differentiation-associated protein;Complex I-B17.2;NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 12;NADH-ubiquinone oxidoreductase subunit B17.2,DAP13;NDUFA12
Q9BQP7,Uncharacterized protein C20orf72;Chromosome 20 open reading frame 72,C20orf72;RP11-504H3.1-002;RP11-504H3.1-003
P28331,"Complex I-75kD;NADH-ubiquinone oxidoreductase 75 kDa subunit, mitochondrial;cDNA FLJ53201, highly similar to NADH-ubiquinone oxidoreductase 75 kDa subunit, mitochondrial (EC 1.6.5.3);cDNA FLJ55879, highly similar to NADH-ubiquinone oxidoreductase 75 kDa subunit, mitochondrial (EC 1.6.5.3);cDNA FLJ60586, highly similar to NADH-ubiquinone oxidoreductase 75 kDa subunit, mitochondrial (EC 1.6.5.3)",NDUFS1
Q9HC36,RNA methyltransferase-like protein 1,HC90;RNMTL1
E7ESL0,"39S ribosomal protein L22, mitochondrial;39S ribosomal protein L25, mitochondrial;cDNA FLJ55384, highly similar to Homo sapiens mitochondrial ribosomal protein L22 (MRPL22), transcript variant 1, mRNA;Putative uncharacterized protein MRPL22",HSPC158;MRPL22;MRPL25;RPML25
Q86U28,"HESB-like domain-containing protein 1;Iron-sulfur cluster assembly 2 homolog, mitochondrial",HBLD1;ISCA2
Q5JRX3,"Pitrilysin metalloproteinase 1;Presequence protease, mitochondrial;Putative uncharacterized protein PITRM1",KIAA1104;MP1;PITRM1
Q9BRJ2,"39S ribosomal protein L45, mitochondrial",MRPL45
Q9BV79,"Nuclear receptor-binding factor 1;Trans-2-enoyl-CoA reductase, mitochondrial",CGI-63;MECR;NBRF1
P20674,"Cytochrome c oxidase polypeptide Va;Cytochrome c oxidase subunit 5A, mitochondrial",COX5A
P51649,"Aldehyde dehydrogenase family 5 member A1;NAD(+)-dependent succinic semialdehyde dehydrogenase;Succinate-semialdehyde dehydrogenase, mitochondrial;Putative uncharacterized protein ALDH5A1",ALDH5A1;SSADH
Q9Y3D9,"28S ribosomal protein S23, mitochondrial",CGI-138;HSPC329;MRPS23
P61604,"10 kDa chaperonin;10 kDa heat shock protein, mitochondrial;Chaperonin 10;Early-pregnancy factor;Heat shock 10kDa protein 1 (Chaperonin 10), isoform CRA_b;Putative uncharacterized protein HSPE1",HSPE1;hCG_21429
Q02218,"2-oxoglutarate dehydrogenase complex component E1;2-oxoglutarate dehydrogenase, mitochondrial;Alpha-ketoglutarate dehydrogenase",OGDH
P17568,Cell adhesion protein SQM1;Complex I-B18;NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 7;NADH-ubiquinone oxidoreductase B18 subunit,NDUFB7
P00390,"Glutathione reductase, mitochondrial;Glutathion reductase delta8 alternative splicing variant;Glutathion reductase delta9 alternative splicing varian;Glutathion reductase delta8+9 alternative splicing variant",GLUR;GRD1;GSR
P00367,"Glutamate dehydrogenase 1, mitochondrial;cDNA FLJ55203, highly similar to Glutamate dehydrogenase 1, mitochondrial (EC 1.4.1.3);cDNA FLJ16138 fis, clone BRALZ2017531, highly similar to Glutamate dehydrogenase 1, mitochondrial (EC 1.4.1.3);Glutamate dehydrogenase 1, isoform CRA_a;Glutamate dehydrogenase 2, mitochondrial",GLUD;GLUD1;hCG_1993805;GLUD2;GLUDP1
P80404,"(S)-3-amino-2-methylpropionate transaminase;4-aminobutyrate aminotransferase, mitochondrial;GABA aminotransferase;Gamma-amino-N-butyrate transaminase;L-AIBAT",ABAT;GABAT
Q13011,"Delta(3,5)-Delta(2,4)-dienoyl-CoA isomerase, mitochondrial",ECH1
Q8N0X4,"Citrate lyase subunit beta-like protein, mitochondrial;cDNA FLJ51306, highly similar to Homo sapiens citrate lyase beta like (CLYBL), transcript variant 2, mRNA",CLB;CLYBL
D6R9U0,Coiled-coil-helix-coiled-coil-helix domain-containing protein 6,CHCHD6
P23786,"Carnitine O-palmitoyltransferase 2, mitochondrial;Carnitine palmitoyltransferase II",CPT1;CPT2
Q8NE22,Uncharacterized protein C5orf35,C5orf35
Q9NVS2,"28S ribosomal protein S18-3, mitochondrial;28S ribosomal protein S18a, mitochondrial;Mitochondrial ribosomal protein S18A;cDNA FLJ52919, highly similar to 28S ribosomal protein S18a, mitochondrial;Mitochondrial ribosomal protein S18A, isoform CRA_b",MRPS18A;RP1-261G23.2-002;hCG_19012;RP1-261G23.2-001
Q8NE62,"Choline dehydrogenase, mitochondrial",CHDH
O94925,"Glutaminase kidney isoform, mitochondrial;K-glutaminase;L-glutamine amidohydrolase",GLS;GLS1;KIAA0838
Q96HJ9,UPF0562 protein C7orf55,C7orf55;HSPC268
Q9NYK5,"39S ribosomal protein L39, mitochondrial;39S ribosomal protein L5, mitochondrial;Putative uncharacterized protein MRPL39",C21orf92;MRPL39;MRPL5;MSTP003;PRED22;RPML5
Q8WWV3,"NOGO-interacting mitochondrial protein;Reticulon-4-interacting protein 1, mitochondrial",NIMP;RTN4IP1
Q99797,Mitochondrial intermediate peptidase,MIP;MIPEP
O43181,"Complex I-18 kDa;Complex I-AQDQ;NADH dehydrogenase [ubiquinone] iron-sulfur protein 4, mitochondrial;NADH-ubiquinone oxidoreductase 18 kDa subunit",NDUFS4
O76031,"ATP-dependent Clp protease ATP-binding subunit clpX-like, mitochondrial;Putative uncharacterized protein DKFZp586J151",CLPX;DKFZp586J151
P82650,"28S ribosomal protein S22, mitochondrial",C3orf5;GK002;MRPS22;RPMS22
O95169,"Complex I-ASHI;NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 8, mitochondrial;NADH-ubiquinone oxidoreductase ASHI subunit;NADH dehydrogenase (Ubiquinone) 1 beta subcomplex, 8, 19kDa;NADH dehydrogenase (Ubiquinone) 1 beta subcomplex, 8, 19kDa, isoform CRA_a;cDNA FLJ52503, highly similar to NADH dehydrogenase (ubiquinone) 1 beta subcomplex subunit 8, mitochondrial (EC 1.6.5.3) (EC 1.6.99.3) (NADH-ubiquinone oxidoreductase ASHI subunit) (Complex I-ASHI) (CI-ASHI)",NDUFB8;hCG_24658;RP11-411B6.5-006;RP11-411B6.5-003
P30084,"Enoyl-CoA hydratase 1;Enoyl-CoA hydratase, mitochondrial;Short-chain enoyl-CoA hydratase",ECHS1
P0C7P0,"CDGSH iron sulfur domain-containing protein 3, mitochondrial;MitoNEET-related protein 2",CISD3
O75306,"Complex I-49kD;NADH dehydrogenase [ubiquinone] iron-sulfur protein 2, mitochondrial;NADH-ubiquinone oxidoreductase 49 kDa subunit;cDNA, FLJ78876, highly similar to NADH-ubiquinone oxidoreductase 49 kDa subunit, mitochondrial (EC 1.6.5.3)",NDUFS2
P40939,"78 kDa gastrin-binding protein;Long chain 3-hydroxyacyl-CoA dehydrogenase;Long-chain enoyl-CoA hydratase;TP-alpha;Trifunctional enzyme subunit alpha, mitochondrial",HADH;HADHA
Q9Y3D3,"28S ribosomal protein S16, mitochondrial;cDNA FLJ58442, highly similar to 28S ribosomal protein S16, mitochondrial (S16mt);Putative uncharacterized protein MRPS16",CGI-132;MRPS16;RPMS16
Q9Y676,"28S ribosomal protein S18-2, mitochondrial;28S ribosomal protein S18b, mitochondrial;Mitochondrial ribosomal protein S18B;Putative uncharacterized protein ENSP00000365691;cDNA FLJ54285, highly similar to 28S ribosomal protein S18b, mitochondrial",C6orf14;HSPC183;MRPS18B;PTD017;DADB-129D20.6-003;DAMA-178G23.8-003;DAMC-83F13.5-003;DAQB-47P19.5-003;DASS-182C6.3-003;XXbac-BCX48F10.3-003;XXbac-BPG249D20.2-003
C9JRZ6,"Putative uncharacterized protein CHCHD3;Coiled-coil-helix-coiled-coil-helix domain containing 3;Coiled-coil-helix-coiled-coil-helix domain containing 3, isoform CRA_d;Coiled-coil-helix-coiled-coil-helix domain-containing protein 3, mitochondrial",CHCHD3;hCG_2014841;tcag7.1158
Q99766,"ATP synthase subunit s, mitochondrial;ATP synthase-coupling factor B;Mitochondrial ATP synthase regulatory component factor B;ATP synthase coupling factor B-like 1",ATP5S;ATPW
Q16134,"Electron transfer flavoprotein-ubiquinone oxidoreductase, mitochondrial;Electron-transferring-flavoprotein dehydrogenase;Putative uncharacterized protein ETFDH",ETFDH
A6NCI0,"Mitochondrial ribosomal protein L42, isoform CRA_e;Putative uncharacterized protein MRPL42;28S ribosomal protein S32, mitochondrial;39S ribosomal protein L31, mitochondrial;39S ribosomal protein L42, mitochondrial",hCG_1647154;MRPL42;HSPC204;MRPL31;MRPS32;PTD007;RPML31
Q96ER9,Coiled-coil domain-containing protein 51,CCDC51
H0YIV9,GatC-like protein;Protein 15E1.2,15E1.2;GATC
Q99714,17-beta-hydroxysteroid dehydrogenase 10;3-hydroxy-2-methylbutyryl-CoA dehydrogenase;3-hydroxyacyl-CoA dehydrogenase type II;3-hydroxyacyl-CoA dehydrogenase type-2;Endoplasmic reticulum-associated amyloid beta-peptide-binding protein;Mitochondrial ribonuclease P protein 2;Short-chain type dehydrogenase/reductase XH98G2;Type II HADH;Hydroxysteroid (17-beta) dehydrogenase 10,ERAB;HADH2;HSD17B10;MRPP2;SCHAD;XH98G2;RP3-339A18.2-004
Q9NUB1,"Acetate--CoA ligase 2;Acetyl-CoA synthetase 2;Acetyl-coenzyme A synthetase 2-like, mitochondrial;Acyl-CoA synthetase short-chain family member 1;cDNA FLJ43068 fis, clone BRTHA3008778, moderately similar to Acetyl-coenzyme A synthetase (EC 6.2.1.1)",ACAS2L;ACSS1;KIAA1846
P13804,"Electron transfer flavoprotein subunit alpha, mitochondrial;cDNA FLJ50859, highly similar to Electron transfer flavoprotein subunit alpha, mitochondrial",ETFA
Q86YH6,"Candidate tumor suppressor protein;Decaprenyl pyrophosphate synthase subunit 2;Decaprenyl-diphosphate synthase subunit 2;cDNA FLJ56514, highly similar to Decaprenyl-diphosphate synthase subunit 2 (EC 2.5.1.-)",C6orf210;DLP1;PDSS2
P31040,"Flavoprotein subunit of complex II;Succinate dehydrogenase [ubiquinone] flavoprotein subunit, mitochondrial",SDH2;SDHA;SDHF
Q9P0J1,"[Pyruvate dehydrogenase [acetyl-transferring]]-phosphatase 1, mitochondrial;Protein phosphatase 2C;Pyruvate dehydrogenase phosphatase catalytic subunit 1",PDP;PDP1;PPM2C
Q9H2K0,"Translation initiation factor IF-3, mitochondrial",DC38;MTIF3
P24539,"ATP synthase subunit b, mitochondrial;ATP synthase, H+ transporting, mitochondrial F0 complex, subunit B1",ATP5F1;RP11-552M11.5-005
O75964,"ATP synthase subunit g, mitochondrial",ATP5L
Q9BYT8,"Angiotensin-binding protein;Microsomal endopeptidase;Mitochondrial oligopeptidase M;Neurolysin, mitochondrial;Neurotensin endopeptidase",AGTBP;KIAA1226;NLN
Q92506,17-beta-hydroxysteroid dehydrogenase 8;3-oxoacyl-[acyl-carrier-protein] reductase;Estradiol 17-beta-dehydrogenase 8;Protein Ke6;Really interesting new gene 2 protein;Testosterone 17-beta-dehydrogenase 8,FABGL;HKE6;HSD17B8;RING2
C9JJ19,"Putative uncharacterized protein MRPS34;28S ribosomal protein S34, mitochondrial",MRPS34
E7EPT4,"NADH dehydrogenase [ubiquinone] flavoprotein 2, mitochondrial;NADH-ubiquinone oxidoreductase 24 kDa subunit",NDUFV2
P82663,"28S ribosomal protein S25, mitochondrial;cDNA FLJ59193, highly similar to Mitochondrial 28S ribosomal protein S25;cDNA FLJ54123, moderately similar to Mitochondrial 28S ribosomal protein S25",MRPS25;RPMS25
Q9BRT2,Breast cancer-associated protein SGA-81M;Uncharacterized protein C6orf125;OTTHUMP00000016217,C6orf125;RP11-6B20.2-002
Q5SXM8,DNL-type zinc finger protein;Chromosome 9 open reading frame 151,C9orf151;DNLZ;RP11-413M3.2-002
Q96I99,"GTP-specific succinyl-CoA synthetase subunit beta;Succinyl-CoA ligase [GDP-forming] subunit beta, mitochondrial;Succinyl-CoA synthetase beta-G chain",SUCLG2
Q9Y2R0,Coiled-coil domain-containing protein 56,CCDC56;HSPC009
Q9HC38,Glyoxalase domain-containing protein 4;cDNA FLJ55095,C17orf25;CGI-150;GLOD4;My027
Q5JTZ9,"Alanine--tRNA ligase;Alanyl-tRNA synthetase-like;Probable alanyl-tRNA synthetase, mitochondrial",AARS2;AARSL;KIAA1270
P82933,"28S ribosomal protein S9, mitochondrial",MRPS9;RPMS9
O00217,"Complex I-23kD;NADH dehydrogenase [ubiquinone] iron-sulfur protein 8, mitochondrial;NADH-ubiquinone oxidoreductase 23 kDa subunit;TYKY subunit",NDUFS8
Q9BYN8,"28S ribosomal protein S13, mitochondrial;28S ribosomal protein S26, mitochondrial",C20orf193;MRPS26;RPMS13
Q9BW91,"Adenosine diphosphoribose pyrophosphatase;ADP-ribose diphosphatase;ADP-ribose phosphohydrolase;ADP-ribose pyrophosphatase, mitochondrial;Nucleoside diphosphate-linked moiety X motif 9",NUDT10;NUDT9;PSEC0099;UNQ3012/PRO9771
Q9NSE4,"Isoleucine--tRNA ligase;Isoleucyl-tRNA synthetase, mitochondrial",IARS2
O75251,"Complex I-20kD;NADH dehydrogenase [ubiquinone] iron-sulfur protein 7, mitochondrial;NADH-ubiquinone oxidoreductase 20 kDa subunit;PSST subunit;Putative uncharacterized protein NDUFS7;cDNA FLJ34304 fis, clone FEBRA2007880, highly similar to NADH-ubiquinone oxidoreductase 20 kDa subunit, mitochondrial (EC 1.6.5.3)",NDUFS7
Q9GZT8,Amyotrophic lateral sclerosis 2 chromosomal region candidate gene 1 protein;NIF3-like protein 1;NIF3L1 isoform beta;NIF3L1 isoform gamma,ALS2CR1;MDS015;My018;NIF3L1
Q6L8Q7,"2,5-phosphodiesterase 12",PDE12
P52758,14.5 kDa translational inhibitor protein;Ribonuclease UK114;UK114 antigen homolog,HRSP12;PSP
Q96GW9,"Methionine--tRNA ligase 2;Methionyl-tRNA synthetase, mitochondrial;Mitochondrial methionine--tRNA ligase;cDNA FLJ51339, highly similar to Methionyl-tRNA synthetase, mitochondrial (EC 6.1.1.10)",MARS2
Q96EY1,"DnaJ homolog subfamily A member 3, mitochondrial;DnaJ protein Tid-1;Hepatocellular carcinoma-associated antigen 57;Tumorous imaginal discs protein Tid56 homolog",DNAJA3;HCA57;TID1
Q16795,"Complex I-39kD;NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 9, mitochondrial;NADH-ubiquinone oxidoreductase 39 kDa subunit",NDUFA9;NDUFS2L
P56556,Complex I-B14;LYR motif-containing protein 6;NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 6;NADH-ubiquinone oxidoreductase B14 subunit,LYRM6;NADHB14;NDUFA6
P24752,"Acetoacetyl-CoA thiolase;Acetyl-CoA acetyltransferase, mitochondrial;T2",ACAT;ACAT1;MAT
P10809,"60 kDa chaperonin;60 kDa heat shock protein, mitochondrial;Chaperonin 60;Heat shock protein 60;HuCHA60;Mitochondrial matrix protein P1;P60 lymphocyte protein",HSP60;HSPD1
P49821,"Complex I-51kD;NADH dehydrogenase [ubiquinone] flavoprotein 1, mitochondrial;NADH dehydrogenase flavoprotein 1;NADH-ubiquinone oxidoreductase 51 kDa subunit;cDNA FLJ57949, highly similar to NADH-ubiquinone oxidoreductase 51 kDa subunit, mitochondrial (EC 1.6.5.3);cDNA, FLJ79021, highly similar to NADH-ubiquinone oxidoreductase 51 kDa subunit, mitochondrial (EC 1.6.5.3)",NDUFV1;UQOR1
P82909,"28S ribosomal protein S36, mitochondrial",DC47;MRPS36
Q8N0V3,"Putative ribosome-binding factor A, mitochondrial",C18orf22
Q7L592,"Protein midA homolog, mitochondrial;Putative uncharacterized protein C2orf56",C2orf56;PRO1853
Q9Y2S7,38 kDa DNA polymerase delta interaction protein;Polymerase delta-interacting protein 2,HSPC017;PDIP38;POLD4;POLDIP2
Q6UB35,"Formyltetrahydrofolate synthetase;Monofunctional C1-tetrahydrofolate synthase, mitochondrial",FTHFSDC1;MTHFD1L
Q9NVS9,"Pyridoxamine-phosphate oxidase;Pyridoxine-5-phosphate oxidase;cDNA FLJ59601, highly similar to Pyridoxine-5-phosphate oxidase (EC 1.4.3.5);cDNA FLJ59109, highly similar to Pyridoxine-5-phosphate oxidase (EC 1.4.3.5);cDNA FLJ59599, highly similar to Pyridoxine-5-phosphate oxidase (EC 1.4.3.5)",PNPO
Q9ULD0,"2-oxoglutarate dehydrogenase complex component E1-like;2-oxoglutarate dehydrogenase-like, mitochondrial;Alpha-ketoglutarate dehydrogenase-like",KIAA1290;OGDHL
Q8NCW5,Apolipoprotein A-I-binding protein;YjeF N-terminal domain-containing protein 1;Apolipoprotein A-I binding protein,AIBP;APOA1BP;YJEFN1;RP11-284F21.3-004
P49247,Phosphoriboisomerase;Ribose-5-phosphate isomerase;Putative uncharacterized protein RPIA,RPI;RPIA
Q7L0Y3,HBV pre-S2 trans-regulated protein 2;Mitochondrial ribonuclease P protein 1;Renal carcinoma antigen NY-REN-49;RNA (guanine-9-)-methyltransferase domain-containing protein 1;Putative uncharacterized protein RG9MTD1,MRPP1;RG9MTD1
O94903,Proline synthase co-transcribed bacterial homolog protein,PROSC
E9PAL9,5-nucleotidase domain-containing protein 2;Putative uncharacterized protein NT5DC2,NT5DC2
B4DRT2,"cDNA FLJ54536, highly similar to Mitochondrial 28S ribosomal protein S27;28S ribosomal protein S27, mitochondrial",KIAA0264;MRPS27
O96000,"Complex I-PDSW;NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 10;NADH-ubiquinone oxidoreductase PDSW subunit;NADH dehydrogenase (Ubiquinone) 1 beta subcomplex, 10, 22kDa, isoform CRA_a;NDUFB10 protein",NDUFB10;hCG_42700
Q6NVY1,"3-hydroxyisobutyryl-CoA hydrolase, mitochondrial;3-hydroxyisobutyryl-coenzyme A hydrolase",HIBCH
Q9Y512,Sorting and assembly machinery component 50 homolog;Transformation-related gene 3 protein,CGI-51;SAMM50;TRG3
O60783,"28S ribosomal protein S14, mitochondrial",MRPS14
Q5TC12,"ATP synthase mitochondrial F1 complex assembly factor 1;ATP11 homolog;Putative uncharacterized protein ATPAF1;cDNA FLJ52027, highly similar to Homo sapiens ATP synthase mitochondrial F1 complex assembly factor 1 (ATPAF1), mRNA;cDNA FLJ50725, highly similar to Homo sapiens ATP synthase mitochondrial F1 complex assembly factor 1 (ATPAF1), mRNA",ATP11;ATPAF1
F2Z2X0,"Nucleoside diphosphate kinase;nm23-H4;Nucleoside diphosphate kinase D;Nucleoside diphosphate kinase, mitochondrial",NME4;Z97634.4-011;NM23D;hCG_1985512;Z97634.4-002
G3V325,"cDNA FLJ76276, highly similar to Homo sapiens pentatricopeptide repeat domain 1 (PTCD1), mRNA;Pentatricopeptide repeat domain 1;Pentatricopeptide repeat-containing protein 1",hCG_2023422;PTCD1;tcag7.1151;KIAA0632
Q9NP81,"Serine--tRNA ligase;SerRSmt;Seryl-tRNA synthetase, mitochondrial;Seryl-tRNA(Ser/Sec) synthetase;cDNA FLJ58521, highly similar to Seryl-tRNA synthetase, mitochondrial (EC 6.1.1.11)",SARS2;SARSM
Q8TAA5,"GrpE protein homolog 2, mitochondrial;Mt-GrpE#2",GRPEL2
O43615,Mitochondrial import inner membrane translocase subunit TIM44,MIMT44;TIM44;TIMM44
Q9NQH7,Aminopeptidase P3;Probable Xaa-Pro aminopeptidase 3,XPNPEP3
P50336,"Protoporphyrinogen oxidase;cDNA FLJ57666, highly similar to Protoporphyrinogen oxidase (EC 1.3.3.4)",PPOX
P07954,"Fumarate hydratase, mitochondrial",FH
P04179,"Superoxide dismutase [Mn], mitochondrial;Superoxide dismutase",SOD2
Q5T2R2,Decaprenyl pyrophosphate synthase subunit 1;Decaprenyl-diphosphate synthase subunit 1;Trans-prenyltransferase;Putative uncharacterized protein PDSS1,DPS1;PDSS1;TPRT
P03915,NADH dehydrogenase subunit 5;NADH-ubiquinone oxidoreductase chain 5,MTND5;MT-ND5;NADH5;ND5
Q9HA77,"Cysteine--tRNA ligase;Probable cysteinyl-tRNA synthetase, mitochondrial",CARS2;OK/SW-cl.10
Q9NVI7,ATPase family AAA domain-containing protein 3A,ATAD3A
Q3SY69,Aldehyde dehydrogenase family 1 member L2;Probable 10-formyltetrahydrofolate dehydrogenase ALDH1L2,ALDH1L2
Q7Z3D6,"UPF0317 protein C14orf159, mitochondrial",C14orf159;UNQ2439/PRO5000
Q6P1X6,UPF0598 protein C8orf82,C8orf82
P13995,"Bifunctional methylenetetrahydrofolate dehydrogenase/cyclohydrolase, mitochondrial;Methenyltetrahydrofolate cyclohydrolase;NAD-dependent methylenetetrahydrofolate dehydrogenase;cDNA FLJ52745, highly similar to Bifunctional methylenetetrahydrofolatedehydrogenase/cyclohydrolase, mitochondrial;Methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 2, methenyltetrahydrofolate cyclohydrolase;Methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 2, methenyltetrahydrofolate cyclohydrolase, isoform CRA_b;Putative uncharacterized protein MTHFD2;cDNA FLJ55007, highly similar to Bifunctional methylenetetrahydrofolate dehydrogenase/cyclohydrolase, mitochondrial",MTHFD2;NMDMC;hCG_40734
P50213,"Isocitrate dehydrogenase [NAD] subunit alpha, mitochondrial;Isocitric dehydrogenase subunit alpha;NAD(+)-specific ICDH subunit alpha",IDH3A
Q969Y2,"Putative uncharacterized protein FASTKD1;GTP-binding protein 3;Mitochondrial GTP-binding protein 1;tRNA modification GTPase GTPBP3, mitochondrial",FASTKD1;GTPBP3;MTGP1
P47985,"Complex III subunit 5;Complex III subunit IX;Cytochrome b-c1 complex subunit 11;Cytochrome b-c1 complex subunit 5;Cytochrome b-c1 complex subunit Rieske, mitochondrial;Rieske iron-sulfur protein;Ubiquinol-cytochrome c reductase 8 kDa protein;Ubiquinol-cytochrome c reductase iron-sulfur subunit;Putative cytochrome b-c1 complex subunit Rieske-like protein 1",UQCRFS1;UQCRFSL1
P08574,"Complex III subunit 4;Complex III subunit IV;Cytochrome b-c1 complex subunit 4;Cytochrome c1, heme protein, mitochondrial;Ubiquinol-cytochrome-c reductase complex cytochrome c1 subunit",CYC1
P30044,"Alu corepressor 1;Antioxidant enzyme B166;Liver tissue 2D-page spot 71B;Peroxiredoxin V;Peroxiredoxin-5, mitochondrial;Peroxisomal antioxidant enzyme;PLP;Thioredoxin peroxidase PMP20;Thioredoxin reductase;TPx type VI;Putative uncharacterized protein PRDX5",ACR1;PRDX5;SBBI10
Q96LL9,DnaJ homolog subfamily C member 30;Williams-Beuren syndrome chromosomal region 18 protein,DNAJC30;WBSCR18
P82932,"28S ribosomal protein S6, mitochondrial",C21orf101;MRPS6;RPMS6
Q9NTG7,"NAD-dependent deacetylase sirtuin-3, mitochondrial;SIR2-like protein 3;cDNA FLJ54618, highly similar to NAD-dependent deacetylase sirtuin-3, mitochondrial (EC 3.5.1.-)",SIR2L3;SIRT3
Q9Y3D2,"Methionine-R-sulfoxide reductase B2, mitochondrial;Methionine sulfoxide reductase B2, isoform CRA_a;Methionine-r-sulfoxide reductase B2 variant 1;Putative uncharacterized protein MSRB2",CBS-1;CGI-131;MSRB;MSRB2;hCG_23087
Q9H7Z7,"Microsomal prostaglandin E synthase 2;Prostaglandin E synthase 2;Prostaglandin E synthase 2 truncated form;Prostaglandin E synthase 2, isoform CRA_c;Putative uncharacterized protein PTGES2",C9orf15;PGES2;PTGES2;hCG_1785478
P03905,NADH dehydrogenase subunit 4;NADH-ubiquinone oxidoreductase chain 4,MTND4;MT-ND4;NADH4;ND4
H0Y886,"Complex I-SGDH;NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 5, mitochondrial;NADH-ubiquinone oxidoreductase SGDH subunit;NADH dehydrogenase (Ubiquinone) 1 beta subcomplex, 5, 16kDa, isoform CRA_h;NDUFB5 protein",NDUFB5;hCG_1787208
P31930,"Complex III subunit 1;Core protein I;Cytochrome b-c1 complex subunit 1, mitochondrial;Ubiquinol-cytochrome-c reductase complex core protein 1",UQCRC1
Q5VTE6,"Protein angel homolog 2;cDNA FLJ50631, highly similar to Homo sapiens angel homolog 2 (Drosophila) (ANGEL2), mRNA",ANGEL2;KIAA0759L
Q86X76,Nitrilase homolog 1;Nitrilase 1,NIT1;RP11-544M22.11-002
Q49AM1,"Mitochondrial transcription termination factor-like protein;mTERF domain-containing protein 3, mitochondrial",MTERFD3
P36776,"Lon protease homolog, mitochondrial;Lon protease-like protein;LONHs;Mitochondrial ATP-dependent protease Lon;Serine protease 15;Lon protease homolog",LONP1;PRSS15
Q7Z6M4,"mTERF domain-containing protein 2;cDNA FLJ59868, highly similar to Homo sapiens MTERF domain containing 2 (MTERFD2), mRNA;Putative uncharacterized protein MTERFD2;cDNA FLJ54914, highly similar to Homo sapiens MTERF domain containing 2 (MTERFD2), mRNA",HSPC096;MTERFD2
Q8IYQ7,Threonine synthase-like 1,THNSL1
O75616,Conserved ERA-like GTPase;ERA-W;GTP-binding protein era homolog,ERAL1;HERA
B4DFQ6,"cDNA FLJ51819, weakly similar to Long-chain-fatty-acid--CoA ligase (EC 6.2.1.3);Acyl-CoA synthetase family member 2, mitochondrial;cDNA FLJ54351, weakly similar to Long-chain-fatty-acid--CoA ligase (EC 6.2.1.3);cDNA FLJ50687, weakly similar to Long-chain-fatty-acid--CoA ligase (EC 6.2.1.3)",ACSF2;UNQ493/PRO1009
Q86UT6,Caterpiller protein 11.3;NLR family member X1;Nucleotide-binding oligomerization domain protein 26;Nucleotide-binding oligomerization domain protein 5;Nucleotide-binding oligomerization domain protein 9,NLRX1;NOD26;NOD5;NOD9
P48735,"ICD-M;IDP;Isocitrate dehydrogenase [NADP], mitochondrial;NADP(+)-specific ICDH;Oxalosuccinate decarboxylase;cDNA FLJ50469, highly similar to Isocitrate dehydrogenase;cDNA, FLJ79287, highly similar to Isocitrate dehydrogenase;cDNA FLJ50654, highly similar to Isocitrate dehydrogenase",IDH2
Q02252,"Aldehyde dehydrogenase family 6 member A1;Methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial",ALDH6A1;MMSDH
O75027,"ATP-binding cassette sub-family B member 7, mitochondrial;ATP-binding cassette transporter 7;cDNA FLJ53391, highly similar to ATP-binding cassette sub-family B member 7, mitochondrial",ABC7;ABCB7
Q96D53,Uncharacterized aarF domain-containing protein kinase 4,ADCK4
Q8NFF5,"FAD pyrophosphorylase;FAD synthase;FAD synthase region;Flavin adenine dinucleotide synthase;FMN adenylyltransferase;Molybdenum cofactor biosynthesis protein-like region;FAD1 flavin adenine dinucleotide synthetase homolog (S. cerevisiae);Fad1, flavin adenine dinucleotide synthetase, homolog (Yeast), isoform CRA_e",FLAD1;PP591;hCG_20019;RP11-307C12.7-004
Q96GK7,Fumarylacetoacetate hydrolase domain-containing protein 2A;Fumarylacetoacetate hydrolase domain-containing protein 2B,CGI-105;FAHD2A;FAHD2B
Q9BQ69,MACRO domain-containing protein 1;Protein LRP16,LRP16;MACROD1
Q9Y375,"Complex I intermediate-associated protein 30, mitochondrial;NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 1",CGI-65;CIA30;NDUFAF1
Q96E11,"Ribosome-recycling factor, mitochondrial;Ribosome-releasing factor, mitochondrial",MRRF
Q99551,"Mitochondrial transcription termination factor 1;Transcription termination factor, mitochondrial;cDNA FLJ51270, highly similar to Transcription termination factor, mitochondrial",MTERF
Q9H5Q4,"Dimethyladenosine transferase 2, mitochondrial;Hepatitis C virus NS5A-transactivated protein 5;Mitochondrial 12S rRNA dimethylase 2;Mitochondrial transcription factor B2;S-adenosylmethionine-6-N, N-adenosyl(rRNA) dimethyltransferase 2",NS5ATP5;TFB2M
Q9NXA8,NAD-dependent deacetylase sirtuin-5;SIR2-like protein 5,SIR2L5;SIRT5
Q9Y697,"Cysteine desulfurase, mitochondrial;cDNA FLJ60737, highly similar to Cysteine desulfurase, mitochondrial (EC 2.8.1.7)",HUSSY-08;NFS1;NIFS
Q969P6,"DNA topoisomerase I, mitochondrial",TOP1MT
Q4G176,"Acyl-CoA synthetase family member 3, mitochondrial",ACSF3;PSEC0197
P04181,"Ornithine aminotransferase, hepatic form;Ornithine aminotransferase, mitochondrial;Ornithine aminotransferase, renal form;Ornithine delta-aminotransferase;Ornithine--oxo-acid aminotransferase;cDNA FLJ57880, highly similar to Ornithine aminotransferase, mitochondrial (EC 2.6.1.13);cDNA, FLJ78846, highly similar to Ornithine aminotransferase, mitochondrial (EC 2.6.1.13);Putative uncharacterized protein DKFZp781A11155",OAT;DKFZp781A11155
P25705,"ATP synthase subunit alpha, mitochondrial;ATP synthase subunit alpha",ATP5A;ATP5A1;ATP5AL2;ATPM
Q96QE5,UPF0629 protein C17orf42,C17orf42
Q6UB28,"Methionine aminopeptidase 1D, mitochondrial",MAP1D
P22830,"Ferrochelatase, mitochondrial;Heme synthase;Protoheme ferro-lyase",FECH
F5H5P2,"2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial;Branched-chain alpha-keto acid dehydrogenase E1 component alpha chain;cDNA FLJ55733, highly similar to 2-oxoisovalerate dehydrogenase alpha subunit, mitochondrial (EC 1.2.4.4)",BCKDHA
O00411,"DNA-directed RNA polymerase, mitochondrial",POLRMT
P46199,"Translation initiation factor IF-2, mitochondrial",MTIF2
Q96EL3,"39S ribosomal protein L53, mitochondrial",MRPL53
Q8IVS2,"[Acyl-carrier-protein] malonyltransferase;Malonyl-CoA-acyl carrier protein transacylase, mitochondrial;Mitochondrial malonyltransferase",MCAT;MT
Q9H0R6,Glutaminyl-tRNA synthase-like protein 1;Glutamyl-tRNA(Gln) amidotransferase subunit A homolog,QRSL1
P09622,"Dihydrolipoamide dehydrogenase;Dihydrolipoyl dehydrogenase, mitochondrial;Glycine cleavage system L protein;Dihydrolipoyl dehydrogenase;cDNA FLJ50515, highly similar to Dihydrolipoyl dehydrogenase, mitochondrial (EC 1.8.1.4)",DLD;GCSL;LAD;PHE3
Q8N0U4,Protein FAM185A;cDNA FLJ55811;Putative uncharacterized protein FAM185A,FAM185A
F5GYX8,ATP synthase subunit s-like protein,ATP5SL
Q9NZB8,Cell migration-inducing gene 11 protein;Molybdenum cofactor biosynthesis protein 1;Molybdenum cofactor biosynthesis protein A;Molybdenum cofactor biosynthesis protein C;Molybdenum cofactor synthesis-step 1 protein A-B,MIG11;MOCS1
Q8TB22,Spermatogenesis-associated protein 20;Sperm-specific protein 411,SPATA20
Q08257,"NADPH:quinone reductase;Quinone oxidoreductase;Zeta-crystallin;Putative uncharacterized protein CRYZ;Crystallin, zeta (Quinone reductase), isoform CRA_a;Putative uncharacterized protein DKFZp686C16101",CRYZ;DKFZp686C16101;hCG_21668
P42765,"3-ketoacyl-CoA thiolase, mitochondrial;Acetyl-CoA acyltransferase;Beta-ketothiolase;Mitochondrial 3-oxoacyl-CoA thiolase;T1",ACAA2
Q9UIJ7,"Adenylate kinase 3;Adenylate kinase 3 alpha-like 1;GTP:AMP phosphotransferase mitochondrial;Adenylate kinase 3, isoform CRA_b;cDNA FLJ40886 fis, clone UTERU2000663, highly similar to GTP:AMP phosphotransferase mitochondrial (EC 2.7.4.10);GTP:AMP phosphotransferase",AK3;AK3L1;AK6;AKL3L;hCG_2011468;RP11-6J24.4-001
Q8NI37,Protein phosphatase PTC7 homolog;T-cell activation protein phosphatase 2C;T-cell activation protein phosphatase 2C-like,PPTC7;TAPP2C
Q05932,"Folylpoly-gamma-glutamate synthetase;Folylpolyglutamate synthase, mitochondrial;Tetrahydrofolylpolyglutamate synthase;Folylpolyglutamate synthase",FPGS;RP11-228B15.1-017;RP11-228B15.1-020;RP11-228B15.1-001
O75439,"Beta-MPP;Mitochondrial-processing peptidase subunit beta;P-52;cDNA FLJ33094 fis, clone TRACH2000703, highly similar to Mitochondrial-processing peptidase subunit beta, mitochondrial (EC 3.4.24.64)",MPPB;PMPCB
O15091,Mitochondrial ribonuclease P protein 3,KIAA0391;MRPP3
Q9UJZ1,"EPB72-like protein 2;Stomatin-like protein 2;cDNA FLJ61039, highly similar to Stomatin-like protein 2",HSPC108;SLP2;STOML2
A6NJ78,Methyltransferase 5 domain-containing protein 1;Probable S-adenosyl-L-methionine-dependent methyltransferase METT5D1,METT5D1
Q15119,"[Pyruvate dehydrogenase [lipoamide]] kinase isozyme 2, mitochondrial;Pyruvate dehydrogenase kinase isoform 2",PDK2
Q16762,Rhodanese;Thiosulfate sulfurtransferase,TST
O75891,10-formyltetrahydrofolate dehydrogenase;Aldehyde dehydrogenase family 1 member L1,ALDH1L1;FTHFD
P06576,"ATP synthase subunit beta, mitochondrial",ATP5B;ATPMB;ATPSB
P48047,"ATP synthase subunit O, mitochondrial;Oligomycin sensitivity conferral protein",ATP5O;ATPO
Q86UY8,5-nucleotidase domain-containing protein 3;GRP94-neighboring nucleotidase,GNN;NT5DC3;TU12B1-TY
P55809,"3-oxoacid-CoA transferase 1;Somatic-type succinyl-CoA:3-oxoacid-CoA-transferase;Succinyl-CoA:3-ketoacid-coenzyme A transferase 1, mitochondrial",OXCT;OXCT1;SCOT
O95822,"Malonyl-CoA decarboxylase, mitochondrial",MLYCD
Q96RR1,"Progressive external ophthalmoplegia 1 protein;T7 gp4-like protein with intramitochondrial nucleoid localization;T7-like mitochondrial DNA helicase;Twinkle protein, mitochondrial",C10orf2;PEO1
A3KMH1,Uncharacterized protein KIAA0564,KIAA0564
A4D0W4,"Aminoadipate-semialdehyde synthase;Aminoadipate-semialdehyde synthase, isoform CRA_a;Alpha-aminoadipic semialdehyde synthase, mitochondrial;LKR/SDH;Lysine ketoglutarate reductase;Saccharopine dehydrogenase",AASS;hCG_33410;tcag7.61
P30049,"ATP synthase subunit delta, mitochondrial;F-ATPase delta subunit",ATP5D
P54098,DNA polymerase subunit gamma-1;Mitochondrial DNA polymerase catalytic subunit;PolG-alpha,MDP1;POLG;POLG1;POLGA
A6NGJ4,"cDNA FLJ45232 fis, clone BRCAN2021718, highly similar to Homo sapiens mitochondrial ribosomal protein L10 (MRPL10), mRNA;Mitochondrial ribosomal protein L10, isoform CRA_b;Putative uncharacterized protein MRPL10;39S ribosomal protein L10, mitochondrial;39S ribosomal protein L8, mitochondrial",hCG_29363;MRPL10;MRPL8;RPML8
P30038,"Aldehyde dehydrogenase family 4 member A1;Delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial;cDNA FLJ54479, highly similar to Delta-1-pyrroline-5-carboxylatedehydrogenase, mitochondrial (EC 1.5.1.12);Mitochondrial aldehyde dehydrogenase 4 family member A1 transcript variant ALDH4A1_v6",ALDH4;ALDH4A1;P5CDH
A8MXV4,"Nucleoside diphosphate-linked moiety X motif 19, mitochondrial",NUDT19
Q8NI60,"aarF domain-containing protein kinase 3;Chaperone activity of bc1 complex-like, mitochondrial;Chaperone, ABC1 activity of bc1 complex homolog (S. pombe);cDNA FLJ33175 fis, clone ADRGL2002392, highly similar to Chaperone-activity of bc1 complex-like, mitochondrial;cDNA FLJ53505, highly similar to Chaperone-activity of bc1 complex-like, mitochondrial",ADCK3;CABC1;PP265;RP5-1087E8.1-002;RP5-1087E8.1-003
E7ERL9,"cDNA FLJ56191, highly similar to Homo sapiens valyl-tRNA synthetase like (VARSL), mRNA;Valine--tRNA ligase;Valyl-tRNA synthetase, mitochondrial;Valyl-tRNA synthetase-like",KIAA1885;VARS2;VARS2L;VARSL
Q9BW92,"Threonine--tRNA ligase;Threonyl-tRNA synthetase, mitochondrial;Threonyl-tRNA synthetase-like 1;cDNA FLJ12528 fis, clone NT2RM4000155, moderately similar to THREONYL-TRNA SYNTHETASE, CYTOPLASMIC (EC 6.1.1.3);Threonyl-tRNA synthetase 2, mitochondrial (Putative);Threonyl-tRNA synthetase-like 1, isoform CRA_b",TARS2;TARSL1;hCG_1999130;RP11-54A4.9-010;RP11-54A4.9-012
Q53R41,FAST kinase domain-containing protein 1,FASTKD1;KIAA1800
Q4J6C6,Prolyl endopeptidase-like;Prolylendopeptidase-like,KIAA0436;PREPL
Q9BUE6,"HESB-like domain-containing protein 2;Iron sulfur assembly protein IscA;Iron-sulfur cluster assembly 1 homolog, mitochondrial",GK004;HBLD2;ISCA1
Q14CZ7,FAST kinase domain-containing protein 3,FASTKD3
Q8NC60,Uncharacterized protein C4orf14,C4orf14
P30837,"Aldehyde dehydrogenase 5;Aldehyde dehydrogenase family 1 member B1;Aldehyde dehydrogenase X, mitochondrial",ALDH1B1;ALDH5;ALDHX
O95363,"Phenylalanine--tRNA ligase;Phenylalanyl-tRNA synthetase, mitochondrial",FARS1;FARS2;HSPC320
P43155,Carnitine acetyltransferase;Carnitine O-acetyltransferase;Putative uncharacterized protein CRAT,CAT1;CRAT
Q6P161,"39S ribosomal protein L54, mitochondrial",MRPL54
Q9Y4W6,AFG3-like protein 2;Paraplegin-like protein;Similar to AFG3 ATPase family gene 3-like 2 (Yeast),AFG3L2
Q96I51,RCC1-like G exchanging factor-like protein;Williams-Beuren syndrome chromosomal region 16 protein,WBSCR16
P16219,"Butyryl-CoA dehydrogenase;Short-chain specific acyl-CoA dehydrogenase, mitochondrial",ACADS
Q7L3T8,"Probable prolyl-tRNA synthetase, mitochondrial;Proline--tRNA ligase",PARS2
O95571,"Ethylmalonic encephalopathy protein 1;Hepatoma subtracted clone one protein;Protein ETHE1, mitochondrial",ETHE1;HSCO
O43488,AFB1 aldehyde reductase 1;Aflatoxin B1 aldehyde reductase member 2;Aldoketoreductase 7;Succinic semialdehyde reductase;Putative uncharacterized protein AKR7A2,AFAR;AFAR1;AKR7;AKR7A2
Q9BQ95,"Evolutionarily conserved signaling intermediate in Toll pathway, mitochondrial;Protein SITPEC",ECSIT
Q9NYY8,FAST kinase domain-containing protein 2,FASTKD2;KIAA0971
Q96RP9,"Elongation factor G 1, mitochondrial;Elongation factor G, mitochondrial;Elongation factor G1;Putative uncharacterized protein GFM1",EFG;EFG1;GFM;GFM1
Q9HAC7,CaiB/baiF CoA-transferase family protein C7orf10;Dermal papilla-derived protein 13;C7orf10 protein;cDNA FLJ53872,C7orf10;DERP13
H0YGP4,"Carbamoyl-phosphate synthase [ammonia], mitochondrial;Carbamoyl-phosphate synthetase I",CPS1
Q13472,DNA topoisomerase 3-alpha;DNA topoisomerase III alpha;DNA topoisomerase,TOP3;TOP3A
P21953,"2-oxoisovalerate dehydrogenase subunit beta, mitochondrial;Branched-chain alpha-keto acid dehydrogenase E1 component beta chain;cDNA, FLJ79444, highly similar to 2-oxoisovalerate dehydrogenase subunit beta, mitochondrial (EC 1.2.4.4)",BCKDHB
Q12931,"Heat shock protein 75 kDa, mitochondrial;TNFR-associated protein 1;Tumor necrosis factor type 1 receptor-associated protein",HSP75;TRAP1
Q15118,"[Pyruvate dehydrogenase [lipoamide]] kinase isozyme 1, mitochondrial;Pyruvate dehydrogenase kinase isoform 1;cDNA FLJ51565, highly similar to Pyruvate dehydrogenase (lipoamide) kinase isozyme 1 (EC 2.7.11.2);cDNA FLJ51566, highly similar to Pyruvate dehydrogenase (lipoamide) kinase isozyme 1 (EC 2.7.11.2)",PDK1
Q8N0Z8,tRNA pseudouridine synthase-like 1;tRNA pseudouridylate synthase-like 1;tRNA-uridine isomerase-like 1,PUSL1
Q96AQ8,"Coiled-coil domain-containing protein 90A, mitochondrial",C6orf79;CCDC90A
Q86Y79,Probable peptidyl-tRNA hydrolase;Putative uncharacterized protein PTRH1,C9orf115;PTRH1
Q8TD30,Alanine aminotransferase 2;Glutamate pyruvate transaminase 2;Glutamic--alanine transaminase 2;Glutamic--pyruvic transaminase 2,AAT2;ALT2;GPT2
Q8NFV4,Abhydrolase domain-containing protein 11;Williams-Beuren syndrome chromosomal region 21 protein,ABHD11;PP1226;WBSCR21
Q92947,"Glutaryl-CoA dehydrogenase, mitochondrial;cDNA FLJ59559, highly similar to Glutaryl-CoA dehydrogenase, mitochondrial (EC 1.3.99.7);cDNA FLJ59956, highly similar to Glutaryl-CoA dehydrogenase, mitochondrial (EC 1.3.99.7)",GCDH
Q6PI48,"Aspartate--tRNA ligase;Aspartyl-tRNA synthetase, mitochondrial",DARS2
Q9UBQ7,Glyoxylate reductase/hydroxypyruvate reductase,GLXR;GRHPR;MSTP035;RP11-397D12.2-004
Q8N3R3,Uncharacterized protein C3orf23,C3orf23
O43837,"Isocitrate dehydrogenase [NAD] subunit beta, mitochondrial;Isocitric dehydrogenase subunit beta;NAD(+)-specific ICDH subunit beta",IDH3B
Q8N4T8,3-oxoacyl-[acyl-carrier-protein] reductase;Carbonyl reductase family member 4;Quinone reductase CBR4,CBR4
O75648,Mitochondrial tRNA-specific 2-thiouridylase 1;MTO2 homolog,MTU1;TRMT1;TRMU
O95900,"Probable tRNA pseudouridine synthase 2;cDNA FLJ52131, highly similar to Homo sapiens TruB pseudouridine (psi) synthase homolog 2 (TRUB2), mRNA",TRUB2
Q9BSH4,Coiled-coil domain-containing protein 44;Translational activator of cytochrome c oxidase 1;Translational activator of mitochondrially-encoded cytochrome c oxidase I,CCDC44;PRO0477;TACO1
Q9NVA1,"Basic FGF-repressed Zic-binding protein;Ubiquinol-cytochrome c reductase complex chaperone CBP3 homolog;Ubiquinol-cytochrome c reductase complex chaperone, CBP3 homolog (Yeast);cDNA FLJ59847, highly similar to Basic FGF-repressed Zic-binding protein;cDNA FLJ55209, highly similar to Basic FGF-repressed Zic-binding protein;cDNA FLJ59833, highly similar to Basic FGF-repressed Zic-binding protein",BZFB;C20orf44;UQCC;RP4-614O4.7-003;RP4-614O4.7-018;RP4-614O4.7-007;RP4-614O4.7-005
P07203,Cellular glutathione peroxidase;Glutathione peroxidase 1,GPX1
Q9BXR0,"Guanine insertion enzyme;Queuine tRNA-ribosyltransferase;tRNA-guanine transglycosylase;cDNA FLJ52927, highly similar to Queuine tRNA-ribosyltransferase (EC 2.4.2.29)",QTRT1;TGT;TGUT
Q6YN16,"Hydroxysteroid dehydrogenase-like protein 2;cDNA FLJ61200, highly similar to Homo sapiens hydroxysteroid dehydrogenase like 2 (HSDL2), mRNA",C9orf99;HSDL2
Q5T9A4,ATPase family AAA domain-containing protein 3B,ATAD3B;KIAA1273
Q6PML9,Human embryonic lung protein;Solute carrier family 30 member 9;Zinc transporter 9,C4orf1;HUEL;SLC30A9
Q9BUB7,"Transmembrane protein 70, mitochondrial",TMEM70
P28838,Cytosol aminopeptidase;Leucine aminopeptidase 3;Leucyl aminopeptidase;Peptidase S;Proline aminopeptidase;Prolyl aminopeptidase,LAP3;LAPEP;PEPS
Q5HYK3,"Ubiquinone biosynthesis methyltransferase COQ5, mitochondrial;cDNA FLJ55122, highly similar to Ubiquinone biosynthesis methyltransferaseCOQ5, mitochondrial (EC 2.1.1.-)",COQ5
Q9H4K7,GTP-binding protein 5;Protein obg homolog 1;GTP binding protein 5 (Putative),GTPBP5;OBGH1;RP5-1005F21.5-001
Q969S9,"Elongation factor G 2, mitochondrial;Elongation factor G2;Ribosome-releasing factor 2, mitochondrial",EFG2;GFM2;MSTP027
Q9Y2Z4,"Tyrosine--tRNA ligase;Tyrosyl-tRNA synthetase, mitochondrial",CGI-04;YARS2
Q13423,"NAD(P) transhydrogenase, mitochondrial;Nicotinamide nucleotide transhydrogenase;Pyridine nucleotide transhydrogenase",NNT
Q8N442,GTP-binding protein GUF1 homolog,GUF1
Q96CB9,"NOL1/NOP2/Sun domain family member 4;Putative methyltransferase NSUN4;cDNA FLJ60253, highly similar to Homo sapiens NOL1/NOP2/Sun domain family, member 4 (NSUN4), mRNA;HCG2031650, isoform CRA_f",NSUN4;hCG_2031650
Q9UKU7,"Activator-recruited cofactor 42 kDa component;Acyl-CoA dehydrogenase family member 8;Isobutyryl-CoA dehydrogenase, mitochondrial;cDNA FLJ55244, highly similar to Acyl-CoA dehydrogenase family member 8, mitochondrial (EC 1.3.99.-);Acyl-Coenzyme A dehydrogenase family, member 8, isoform CRA_a;cDNA FLJ90159 fis, clone HEMBB1002465, weakly similar to ACYL-COA DEHYDROGENASE (EC 1.3.99.-);cDNA FLJ59096, highly similar to Acyl-CoA dehydrogenase family member 8, mitochondrial (EC 1.3.99.-)",ACAD8;ARC42;IBD;hCG_37259
G3V5T0,"Glutathione S-transferase zeta 1;GSTZ1-1;Maleylacetoacetate isomerase;Glutathione transferase zeta 1 (Maleylacetoacetate isomerase), isoform CRA_b;Putative uncharacterized protein GSTZ1",GSTZ1;MAAI;hCG_22265
Q7L8L6,FAST kinase domain-containing protein 5,FASTKD5;KIAA1792
Q5T160,"Arginine--tRNA ligase;Arginyl-tRNA synthetase-like;Probable arginyl-tRNA synthetase, mitochondrial",RARS2;RARSL
Q07021,"Complement component 1 Q subcomponent-binding protein, mitochondrial;GC1q-R protein;Glycoprotein gC1qBP;Hyaluronan-binding protein 1;Mitochondrial matrix protein p32;p33",C1QBP;GC1QBP;HABP1;SF2P32
P36551,"Coproporphyrinogen-III oxidase, mitochondrial",CPO;CPOX;CPX
Q15031,"Leucine--tRNA ligase;Probable leucyl-tRNA synthetase, mitochondrial",KIAA0028;LARS2
Q6P1L8,"39S ribosomal protein L14, mitochondrial;39S ribosomal protein L32, mitochondrial",MRPL14;MRPL32;RPML32
Q9H845,"Acyl-CoA dehydrogenase family member 9, mitochondrial",ACAD9
Q5JPH6,"Glutamate--tRNA ligase;Probable glutamyl-tRNA synthetase, mitochondrial",EARS2;KIAA1970
Q9BXW7,Cat eye syndrome critical region protein 5,CECR5
Q8WV93,Lactation elevated protein 1,AFG1;LACE1
E9PI62,GTP-binding protein 7;Mitochondrial GTPase 1,GTPBP7;MTG1
F8WEC0,"Methylmalonic aciduria and homocystinuria type D protein, mitochondrial",C2orf25;CL25022;HSPC161;MMADHC;My011
Q9NVV4,"mtPAP;PAP-associated domain-containing protein 1;Poly(A) RNA polymerase, mitochondrial;Polynucleotide adenylyltransferase;Terminal uridylyltransferase 1",MTPAP;PAPD1
Q9HBH1,"Peptide deformylase, mitochondrial;Polypeptide deformylase",PDF;PDF1A
Q9BT30,Alkylated DNA repair protein alkB homolog 7;Probable alpha-ketoglutarate-dependent dioxygenase ABH7;Spermatogenesis cell proliferation-related protein;Spermatogenesis-associated protein 11,ABH7;ALKBH7;SPATA11;UNQ6002/PRO34564
Q8WV74,"Nucleoside diphosphate-linked moiety X motif 8, mitochondrial",NUDT8
P45954,"2-methyl branched chain acyl-CoA dehydrogenase;2-methylbutyryl-coenzyme A dehydrogenase;Short/branched chain specific acyl-CoA dehydrogenase, mitochondrial;cDNA FLJ57418, highly similar to Short/branched chain specific acyl-CoAdehydrogenase, mitochondrial (EC 1.3.99.-)",ACADSB
Q9H3H1,"hGRO1;Isopentenyl-diphosphate:tRNA isopentenyltransferase;tRNA dimethylallyltransferase, mitochondrial;tRNA isopentenyltransferase;tRNA isopentenyltransferase 1",IPT;MOD5;TRIT1;RP1-118J21.3-003
Q9Y2Z9,"Ubiquinone biosynthesis monooxygenase COQ6;cDNA FLJ50973, highly similar to Ubiquinone biosynthesis monooxygenase COQ6 (EC 1.14.13.-);Coenzyme Q6 homolog, monooxygenase (Yeast), isoform CRA_c;Full-length cDNA clone CS0DM001YP16 of Fetal liver of Homo sapiens (human)",CGI-10;COQ6;hCG_21715
Q969Z0,Cell cycle progression restoration protein 2;FAST kinase domain-containing protein 4;Protein TBRG4;Transforming growth factor beta regulator 4;Putative uncharacterized protein TBRG4,CPR2;FASTKD4;KIAA0948;TBRG4
P49419,Aldehyde dehydrogenase family 7 member A1;Alpha-aminoadipic semialdehyde dehydrogenase;Antiquitin-1;Betaine aldehyde dehydrogenase;Delta1-piperideine-6-carboxylate dehydrogenase,ALDH7A1;ATQ1
Q15120,"[Pyruvate dehydrogenase [lipoamide]] kinase isozyme 3, mitochondrial;Pyruvate dehydrogenase kinase isoform 3",PDK3
Q7Z4G4,tRNA guanosine-2-O-methyltransferase TRM11 homolog,C6orf75;MDS024;TRMT11
B1ANH1,Guanylate kinase 1;GMP kinase;Guanylate kinase,GUK1;RP11-520H14.2-010;RP11-520H14.2-027;RP11-520H14.2-003;RP11-520H14.2-018;RP11-520H14.2-023;GMK;RP11-520H14.2-030;RP11-520H14.2-019
Q9P2R7,"ATP-specific succinyl-CoA synthetase subunit beta;Renal carcinoma antigen NY-REN-39;Succinyl-CoA ligase [ADP-forming] subunit beta, mitochondrial;Succinyl-CoA synthetase beta-A chain;Succinate-CoA ligase, ADP-forming, beta subunit",SUCLA2;RP11-528D24.2-010
Q9Y2Z2,"Protein MTO1 homolog, mitochondrial",CGI-02;MTO1
A6NNL5,Uncharacterized protein C15orf61,C15orf61
Q9BQ52,"ElaC homolog protein 2;Heredity prostate cancer protein 2;Ribonuclease Z 2;tRNA 3 endonuclease 2;tRNase Z 2;Zinc phosphodiesterase ELAC protein 2;cDNA FLJ59369, highly similar to Zinc phosphodiesterase ELAC protein 2 (EC 3.1.26.11)",ELAC2;HPC2
G3XAJ0,Acyl-CoA dehydrogenase family member 10,ACAD10
Q6P087,RNA pseudouridylate synthase domain-containing protein 3;Putative uncharacterized protein RPUSD3,RPUSD3
Q8N465,"D-2-hydroxyglutarate dehydrogenase, mitochondrial;cDNA FLJ61087, highly similar to D-2-hydroxyglutarate dehydrogenase, mitochondrial (EC 1.1.99.-);Putative uncharacterized protein D2HGDH",D2HGD;D2HGDH
P51553,"Isocitrate dehydrogenase [NAD] subunit gamma, mitochondrial;Isocitric dehydrogenase subunit gamma;NAD(+)-specific ICDH subunit gamma",IDH3G
Q9H649,NOL1/NOP2/Sun domain family member 3;Putative methyltransferase NSUN3,MSTP077;NSUN3;UG0651E06
O75879,"Cytochrome oxidase assembly factor PET112 homolog;Probable glutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial",HSPC199;PET112;PET112L
P25325,3-mercaptopyruvate sulfurtransferase;Mercaptopyruvate sulfurtransferase,MPST;TST2;LL22NC01-146D10.4-005
Q9NPE2,Mesenchymal stem cell protein DSC92;Neugrin;Neurite outgrowth-associated protein;Spinal cord-derived protein FI58G,FI58G;HT020;NGRN
Q6P1S2,"Uncharacterized protein C3orf33;cDNA FLJ31139 fis, clone IMR322001185;Chromosome 3 open reading frame 33, isoform CRA_b",C3orf33;MSTP052;hCG_27946
O75570,"Peptide chain release factor 1, mitochondrial;cDNA FLJ55831, highly similar to Peptide chain release factor 1, mitochondrial",MTRF1
Q9P2J9,"[Pyruvate dehydrogenase [acetyl-transferring]]-phosphatase 2, mitochondrial;Pyruvate dehydrogenase phosphatase catalytic subunit 2",KIAA1348;PDP2
Q7Z4W1,Carbonyl reductase II;Dicarbonyl/L-xylulose reductase;Kidney dicarbonyl reductase;L-xylulose reductase;Sperm surface protein P34H,DCXR
Q3KQZ1,Solute carrier family 25 member 35,SLC25A35
Q9H4B0,O-sialoglycoprotein endopeptidase-like protein 1;Probable O-sialoglycoprotein endopeptidase 2,OSGEPL1
P22695,"Complex III subunit 2;Core protein II;Cytochrome b-c1 complex subunit 2, mitochondrial;Ubiquinol-cytochrome-c reductase complex core protein 2",UQCRC2
P08559,"PDHE1-A type I;Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial;cDNA FLJ59461, highly similar to Pyruvate dehydrogenase E1 component alpha subunit, somatic form, mitochondrial (EC 1.2.4.1);Mitochondrial PDHA1;cDNA FLJ54787, highly similar to Pyruvate dehydrogenase E1 component alpha subunit, somatic form, mitochondrial (EC 1.2.4.1);cDNA FLJ52314, highly similar to Pyruvate dehydrogenase E1 component alpha subunit, somatic form, mitochondrial (EC 1.2.4.1)",PDHA1;PHE1A
E7ETE0,Methyltransferase-like protein 8;Putative uncharacterized protein METTL8,METTL8
P49189,"4-trimethylaminobutyraldehyde dehydrogenase;Aldehyde dehydrogenase E3 isozyme;Aldehyde dehydrogenase family 9 member A1;Gamma-aminobutyraldehyde dehydrogenase;R-aminobutyraldehyde dehydrogenase;cDNA FLJ51658, highly similar to 4-trimethylaminobutyraldehyde dehydrogenase (EC 1.2.1.47);cDNA FLJ61765, highly similar to 4-trimethylaminobutyraldehyde dehydrogenase(EC 1.2.1.47)",ALDH4;ALDH7;ALDH9;ALDH9A1
O14874,"[3-methyl-2-oxobutanoate dehydrogenase [lipoamide]] kinase, mitochondrial;Branched-chain alpha-ketoacid dehydrogenase kinase;Branched chain ketoacid dehydrogenase kinase, isoform CRA_c;Putative uncharacterized protein BCKDK;BCKDK protein;Branched chain ketoacid dehydrogenase kinase, isoform CRA_a",BCKDK;hCG_21145
Q15070,Hsa;Mitochondrial inner membrane protein OXA1L;OXA1Hs;Oxidase assembly 1-like protein,OXA1L
O75521,"Delta(3),delta(2)-enoyl-CoA isomerase;Diazepam-binding inhibitor-related protein 1;Dodecenoyl-CoA isomerase;DRS-1;Hepatocellular carcinoma-associated antigen 88;Peroxisomal 3,2-trans-enoyl-CoA isomerase;Renal carcinoma antigen NY-REN-1",DRS1;HCA88;PECI
B4DHX5,"cDNA FLJ53329, highly similar to NADPH:adrenodoxin oxidoreductase, mitochondrial (EC 1.18.1.2);Ferredoxin--NADP(+) reductase;NADPH:adrenodoxin oxidoreductase, mitochondrial;cDNA FLJ54567, highly similar to NADPH:adrenodoxin oxidoreductase, mitochondrial (EC 1.18.1.2)",ADXR;FDXR
Q96DP5,"Methionyl-tRNA formyltransferase, mitochondrial",FMT;FMT1;MTFMT
Q8WVM0,"Dimethyladenosine transferase 1, mitochondrial;Mitochondrial 12S rRNA dimethylase 1;Mitochondrial transcription factor B1;S-adenosylmethionine-6-N, N-adenosyl(rRNA) dimethyltransferase 1",CGI-75;TFB1M
P43897,"Elongation factor Ts, mitochondrial;Elongation factor Ts",TSFM
Q13686,Alkylated DNA repair protein alkB homolog 1;Alpha-ketoglutarate-dependent dioxygenase ABH1;DNA lyase ABH1,ABH;ABH1;ALKBH;ALKBH1
Q16775,"Glyoxalase II;Hydroxyacylglutathione hydrolase, mitochondrial",GLO2;HAGH;HAGH1
Q16740,"Endopeptidase Clp;Putative ATP-dependent Clp protease proteolytic subunit, mitochondrial",CLPP
F5H620,Oxidoreductase NAD-binding domain-containing protein 1,OXNAD1
O43824,Pseudoautosomal GTP-binding protein-like;Putative GTP-binding protein 6,GTPBP6;PGPL
O75880,"Protein SCO1 homolog, mitochondrial;Putative uncharacterized protein SCO1",SCO1;SCOD1
P58557,Putative metalloprotease C21orf57,C21orf57
P09417,"Dihydropteridine reductase;HDHPR;Quinoid dihydropteridine reductase;cDNA FLJ42391 fis, clone 3NB692002806, highly similar to Dihydropteridine reductase (EC 1.5.1.34);Quinoid dihydropteridine reductase, isoform CRA_e;cDNA FLJ55000, highly similar to Dihydropteridine reductase (EC 1.5.1.34);Quinoid dihydropteridine reductase, isoform CRA_c",DHPR;QDPR;hCG_39606
Q9Y606,tRNA pseudouridine synthase A;tRNA pseudouridylate synthase I;tRNA-uridine isomerase I,PP8985;PUS1
Q9HA92,"Oxygen-independent coproporphyrinogen-III oxidase-like protein RSAD1;Radical S-adenosyl methionine domain-containing protein 1, mitochondrial",RSAD1
Q96CM3,RNA pseudouridylate synthase domain-containing protein 4,RPUSD4
P49590,"Histidine--tRNA ligase;Histidine--tRNA ligase-like;Probable histidyl-tRNA synthetase, mitochondrial;cDNA FLJ50406, highly similar to Histidyl-tRNA synthetase homolog (EC 6.1.1.21);Histidyl-tRNA synthetase-like, isoform CRA_a;Putative uncharacterized protein HARS2;cDNA FLJ50611, highly similar to Histidyl-tRNA synthetase homolog (EC 6.1.1.21)",HARS2;HARSL;HARSR;HO3;hCG_1982406
Q9H9P8,"Duranin;L-2-hydroxyglutarate dehydrogenase, mitochondrial;Putative uncharacterized protein L2HGDH",C14orf160;L2HGDH
Q9NPL8,Protein M5-14;Transmembrane protein C3orf1;Putative uncharacterized protein C3orf1,C3orf1;UNQ247/PRO284
P00403,Cytochrome c oxidase polypeptide II;Cytochrome c oxidase subunit 2,COII;COXII;MTCO2;MT-CO2
Q13057,Bifunctional coenzyme A synthase;Dephospho-CoA kinase;Dephospho-CoA pyrophosphorylase;Dephosphocoenzyme A kinase;NBP;Pantetheine-phosphate adenylyltransferase;Phosphopantetheine adenylyltransferase;POV-2,COASY;PSEC0106
Q9NUL7,Mitochondrial DEAD box protein 28;Probable ATP-dependent RNA helicase DDX28,DDX28;MDDX28
P49411,"Elongation factor Tu, mitochondrial;P43",TUFM
Q9NRK6,"ATP-binding cassette sub-family B member 10, mitochondrial;ATP-binding cassette transporter 10;Mitochondrial ATP-binding cassette 2",ABCB10
O60930,Ribonuclease H type II;Ribonuclease H1,RNASEH1;RNH1
Q8WUK0,Phosphoinositide lipid phosphatase;Protein-tyrosine phosphatase mitochondrial 1;PTEN-like phosphatase,MOSP;PLIP;PNAS-129;PTPMT1
P14735,Abeta-degrading protease;Insulin protease;Insulin-degrading enzyme;Insulysin,IDE
A4D1E9,GTP-binding protein 10;Protein obg homolog 2;Putative uncharacterized protein GTPBP10,GTPBP10;OBGH2;UG0751c10
Q16698,"2,4-dienoyl-CoA reductase [NADPH];2,4-dienoyl-CoA reductase, mitochondrial;cDNA FLJ50204, highly similar to 2,4-dienoyl-CoA reductase, mitochondrial (EC 1.3.1.34)",DECR;DECR1
Q02338,"3-hydroxybutyrate dehydrogenase;D-beta-hydroxybutyrate dehydrogenase, mitochondrial;Putative uncharacterized protein BDH1",BDH;BDH1
Q9Y399,"28S ribosomal protein S2, mitochondrial;Mitochondrial ribosomal protein S2",CGI-91;MRPS2;RP11-426A6.2-007
E7ENH9,"ATP-citrate (pro-S-)-lyase;ATP-citrate synthase;Citrate cleavage enzyme;cDNA FLJ55447, highly similar to ATP-citrate synthase (EC 2.3.3.8)",ACLY
Q96C36,Pyrroline-5-carboxylate reductase 2,PYCR2
P82675,"28S ribosomal protein S5, mitochondrial",MRPS5
P22234,AIR carboxylase;Multifunctional protein ADE2;Phosphoribosylaminoimidazole carboxylase;Phosphoribosylaminoimidazole-succinocarboxamide synthase;SAICAR synthetase,ADE2;AIRC;PAICS;PAIS
Q6IN84,"Mitochondrial large ribosomal RNA ribose methylase;rRNA methyltransferase 1, mitochondrial",MRM1
Q9UK39,CCR4 protein homolog;Nocturnin,CCR4;CCRN4L;NOC
Q96GJ1,TRM2 homolog;tRNA (uracil-5-)-methyltransferase homolog,CXorf34;TRMT2B
Q8TBP6,Mitochondrial carrier family protein;Solute carrier family 25 member 40,MCFP;SLC25A40
Q9BSK2,Bone marrow stromal cell mitochondrial carrier protein;Protein PNC1;Solute carrier family 25 member 33,SLC25A33
Q96CU9,FAD-dependent oxidoreductase domain-containing protein 1;cDNA FLJ52799,FOXRED1;FP634
Q330K2,"Putative phytoene synthase;UPF0551 protein C8orf38, mitochondrial",C8orf38
Q8N3Z3,GTP-binding protein 8;GTP-binding protein 8.,GTPBP8
Q9BTZ2,Dehydrogenase/reductase SDR family member 4;NADPH-dependent carbonyl reductase/NADP-retinol dehydrogenase;NADPH-dependent retinol dehydrogenase/reductase;Peroxisomal short-chain alcohol dehydrogenase;SCAD-SRL;Short-chain dehydrogenase/reductase family member 4;Putative uncharacterized protein DHRS4L2,DHRS4;UNQ851/PRO1800;DHRS4L2
Q9H2D1,"Mitochondrial folate transporter/carrier;Solute carrier family 25 member 32;cDNA FLJ53610, highly similar to Mitochondrial folate transporter/carrier",MFT;MFTC;SLC25A32
Q8N5M1,ATP synthase mitochondrial F1 complex assembly factor 2;ATP12 homolog;Putative uncharacterized protein ATPAF2,ATP12;ATPAF2;LP3663
P56134,"ATP synthase subunit f, mitochondrial;ATP synthase, H+ transporting, mitochondrial F0 complex, subunit f, isoform 2;ATP synthase, H+ transporting, mitochondrial F0 complex, subunit F2;ATP5J2 protein",ATP5J2;ATP5JL;hCG_2023419;tcag7.652
O75330,Hyaluronan mediated motility receptor;Intracellular hyaluronic acid-binding protein;Receptor for hyaluronan-mediated motility,HMMR;IHABP;RHAMM
O75746,"Calcium-binding mitochondrial carrier protein Aralar1;Mitochondrial aspartate glutamate carrier 1;Solute carrier family 25 member 12;cDNA FLJ33752 fis, clone BRCAN2000364, highly similar to Calcium-binding mitochondrial carrier protein Aralar1",ARALAR1;SLC25A12
Q8WV60,"Pentatricopeptide repeat-containing protein 2;cDNA FLJ50338, highly similar to Homo sapiens pentatricopeptide repeat domain 2 (PTCD2), mRNA;cDNA FLJ55874, highly similar to Homo sapiens pentatricopeptide repeat domain 2 (PTCD2), mRNA",PTCD2
P11177,"Pyruvate dehydrogenase E1 component subunit beta, mitochondrial;cDNA FLJ52988, highly similar to Pyruvate dehydrogenase E1 component subunit beta, mitochondrial (EC 1.2.4.1);Putative uncharacterized protein PDHB",PDHB;PHE1B
O95714,HECT domain and RCC1-like domain-containing protein 2;Probable E3 ubiquitin-protein ligase HERC2,HERC2
O14949,Complex III subunit 8;Complex III subunit VIII;Cytochrome b-c1 complex subunit 8;Ubiquinol-cytochrome c reductase complex 9.5 kDa protein;Ubiquinol-cytochrome c reductase complex ubiquinone-binding protein QP-C,UQCRQ
Q9HCC0,"3-methylcrotonyl-CoA carboxylase 2;3-methylcrotonyl-CoA carboxylase non-biotin-containing subunit;3-methylcrotonyl-CoA:carbon dioxide ligase subunit beta;Methylcrotonoyl-CoA carboxylase beta chain, mitochondrial",MCCB;MCCC2
Q9NWR8,Coiled-coil domain-containing protein 109B,CCDC109B
Q6NUK1,Calcium-binding mitochondrial carrier protein SCaMC-1;Mitochondrial ATP-Mg/Pi carrier protein 1;Mitochondrial Ca(2+)-dependent solute carrier protein 1;Small calcium-binding mitochondrial carrier protein 1;Solute carrier family 25 member 24,APC1;MCSC1;SCAMC1;SLC25A24
Q9BVL4,Selenoprotein O,SELO
O95168,"Complex I-B15;NADH dehydrogenase [ubiquinone] 1 beta subcomplex subunit 4;NADH-ubiquinone oxidoreductase B15 subunit;NADH dehydrogenase (Ubiquinone) 1 beta subcomplex, 4, 15kDa;Putative uncharacterized protein NDUFB4",NDUFB4
Q9NWS8,Required for meiotic nuclear division protein 1 homolog;Required for meiotic nuclear division 1 homolog (S. cerevisiae),C6orf96;RMND1;RP11-351K16.6-006
P35270,Sepiapterin reductase,SPR
C9J2U4,"Chromosome 3 open reading frame 31, isoform CRA_f;Putative uncharacterized protein C3orf31;cDNA FLJ60579;MMP37-like protein, mitochondrial",C3orf31;hCG_28045
P12532,"Acidic-type mitochondrial creatine kinase;Creatine kinase U-type, mitochondrial;Ubiquitous mitochondrial creatine kinase",CKMT;CKMT1A;CKMT1B
B4DMU0,"Pyrroline-5-carboxylate reductase;Pyrroline-5-carboxylate reductase 1, mitochondrial",PYCR1;hCG_38803
Q96R06,Astrin;Deepest;Mitotic spindle-associated protein p126;Sperm-associated antigen 5,SPAG5
Q9ULM3,YEATS domain-containing protein 2,KIAA1197;YEATS2
P82914,"28S ribosomal protein S15, mitochondrial",DC37;MRPS15;RPMS15
Q8N4Q0,"Zinc-binding alcohol dehydrogenase domain-containing protein 2;cDNA FLJ52809, highly similar to Zinc-binding alcohol dehydrogenasedomain-containing protein 2 (EC 1.-.-.-)",ZADH2
P54819,"Adenylate kinase 2, mitochondrial;ATP-AMP transphosphorylase 2",ADK2;AK2
Q86WA6,Biphenyl hydrolase-like protein;Biphenyl hydrolase-related protein;Breast epithelial mucin-associated antigen;Valacyclovir hydrolase,BPHL;MCNAA
Q86U90,"Dopamine receptor-interacting protein 3;Ischemia/reperfusion-inducible protein homolog;YrdC domain-containing protein, mitochondrial",DRIP3;IRIP;YRDC
P29353,"SHC-transforming protein 1;SHC-transforming protein 3;SHC-transforming protein A;Src homology 2 domain-containing-transforming protein C1;cDNA FLJ56101, highly similar to SHC-transforming protein 1",SHC;SHC1;SHCA
Q8TB37,"Nucleotide-binding protein-like;cDNA FLJ59772, highly similar to Nucleotide-binding protein-like",C14orf127;NUBPL
E2QC23,"2-amino-3-ketobutyrate coenzyme A ligase, mitochondrial;Aminoacetone synthase;Glycine acetyltransferase",GCAT;KBL
P55084,"3-ketoacyl-CoA thiolase;Acetyl-CoA acyltransferase;Beta-ketothiolase;TP-beta;Trifunctional enzyme subunit beta, mitochondrial;cDNA FLJ56214, highly similar to Trifunctional enzyme subunit beta, mitochondrial;Putative uncharacterized protein HADHB",HADHB;MSTP029
Q12888,Tumor suppressor p53-binding protein 1;Putative uncharacterized protein TP53BP1,TP53BP1
Q15046,Lysine--tRNA ligase;Lysyl-tRNA synthetase,KARS;KIAA0070
Q9UI30,TRM112-like protein;tRNA methyltransferase 112 homolog,AD-001;HSPC152;HSPC170;TRMT112
P53597,"Succinyl-CoA ligase [GDP-forming] subunit alpha, mitochondrial;Succinyl-CoA synthetase subunit alpha",SUCLG1
Q96JN8,Neuralized-like protein 4,KIAA1787;NEURL4
Q8WWC4,"Uncharacterized protein C2orf47, mitochondrial",C2orf47
Q546F9,"Mitochondrial aspartate-glutamate carrier protein;Solute carrier family 25, member 13 (Citrin), isoform CRA_a;Calcium-binding mitochondrial carrier protein Aralar2;Citrin;Mitochondrial aspartate glutamate carrier 2;Solute carrier family 25 member 13",hCG_40633;SLC25A13;ARALAR2
Q8NE86,Coiled-coil domain-containing protein 109A,C10orf42;CCDC109A
P49321,"Nuclear autoantigenic sperm protein;cDNA FLJ53176, highly similar to Nuclear autoantigenic sperm protein",NASP
Q9Y2R5,"28S ribosomal protein S17, mitochondrial",HSPC011;MRPS17;RPMS17
Q9UI43,Protein ftsJ homolog 2;Putative ribosomal RNA methyltransferase 2;rRNA (uridine-2-O-)-methyltransferase,FJH1;FTSJ2
O15042,140 kDa Ser/Arg-rich domain protein;U2-associated protein SR140;Putative uncharacterized protein ENSP00000417441,KIAA0332;SR140
Q92576,PHD finger protein 3,KIAA0244;PHF3
Q9H300,"Mitochondrial intramembrane cleaving protease PARL;P-beta;Presenilins-associated rhomboid-like protein, mitochondrial;Putative uncharacterized protein PARL",PARL;PRO2207;PSARL
Q15047,ERG-associated protein with SET domain;Histone H3-K9 methyltransferase 4;Histone-lysine N-methyltransferase SETDB1;Lysine N-methyltransferase 1E;SET domain bifurcated 1,KIAA0067;KMT1E;SETDB1
Q92734,Protein TFG;TRK-fused gene protein;TFG protein;Putative uncharacterized protein TFG,TFG
Q6NZY4,Zinc finger CCHC domain-containing protein 8,ZCCHC8
Q9Y3B7,"39S ribosomal protein L11, mitochondrial;Mitochondrial ribosomal protein L11, isoform CRA_c;Putative uncharacterized protein MRPL11",CGI-113;MRPL11;hCG_2017204
Q5UIP0,Rap1-interacting factor 1 homolog;Telomere-associated protein RIF1,RIF1
P38432,Coilin;p80,CLN80;COIL
P09543,"2,3-cyclic-nucleotide 3-phosphodiesterase",CNP
O95861,"3(2),5-bisphosphate nucleotidase 1;Bisphosphate 3-nucleotidase 1;PAP-inositol-1,4-phosphatase;cDNA FLJ52417, highly similar to 3(2),5-bisphosphate nucleotidase 1 (EC 3.1.3.7);Putative uncharacterized protein BPNT1;cDNA FLJ52203, highly similar to 3(2),5-bisphosphate nucleotidase 1 (EC 3.1.3.7)",BPNT1
Q96S59,"BPM90;BPM-L;Ran-binding protein 9;Ran-binding protein M;RanBP7;cDNA, FLJ93856, Homo sapiens RAN binding protein 9 (RANBP9), mRNA",RANBP9;RANBPM
E7EQZ4,"Component of gems 1;Gemin-1;Survival motor neuron protein;cDNA FLJ60754, moderately similar to Survival motor neuron protein",SMN;SMN1;SMN2;SMNC;SMNT
Q9NPJ3,Acyl-coenzyme A thioesterase 13;Thioesterase superfamily member 2,ACOT13;HT012;PNAS-27;THEM2
A6NHB5,Putative uncharacterized protein ZMYM3;Zinc finger MYM-type protein 3;Zinc finger protein 261,ZMYM3;DXS6673E;KIAA0385;ZNF261
Q9Y2Q9,"28S ribosomal protein S28, mitochondrial;28S ribosomal protein S35, mitochondrial",HSPC007;MRPS28;MRPS35
O43149,Zinc finger ZZ-type and EF-hand domain-containing protein 1,KIAA0399;ZZEF1
Q8N3X1,Formin-binding protein 30;Formin-binding protein 4,FBP30;FNBP4;KIAA1014
F5H039,Domain E;Domain G;Gephyrin;Molybdopterin adenylyltransferase;Molybdopterin molybdenumtransferase,GPH;GPHN;KIAA1385
Q14444,Caprin-1;Cell cycle-associated protein 1;Cytoplasmic activation- and proliferation-associated protein 1;GPI-anchored membrane protein 1;GPI-anchored protein p137;Membrane component chromosome 11 surface marker 1,CAPRIN1;GPIAP1;GPIP137;M11S1
Q9NYZ3,G2 and S phase-expressed protein 1;Protein B99 homolog,GTSE1
Q9NX74,tRNA-dihydrouridine synthase 2-like;Up-regulated in lung cancer protein 8,DUS2;DUS2L
P40222,Alpha-taxilin,TXLN;TXLNA
Q9P0J0,Cell death regulatory protein GRIM-19;Complex I-B16.6;Gene associated with retinoic and interferon-induced mortality 19 protein;NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 13;NADH-ubiquinone oxidoreductase B16.6 subunit,CDA016;CGI-39;GRIM19;NDUFA13
O75431,"Metaxin-2;Mitochondrial outer membrane import complex protein 2;cDNA FLJ51595, highly similar to Metaxin-2;Metaxin 2;Metaxin 2, isoform CRA_c;Putative uncharacterized protein MTX2",MTX2;hCG_1778458
Q9H9B1,"Euchromatic histone-lysine N-methyltransferase 1;G9a-like protein 1;Histone H3-K9 methyltransferase 5;Histone-lysine N-methyltransferase, H3 lysine-9 specific 5;Lysine N-methyltransferase 1D;Putative uncharacterized protein EHMT1",EHMT1;EUHMTASE1;KIAA1876;KMT1D
Q9NTX5,Enoyl-CoA hydratase domain-containing protein 1,ECHDC1
P12270,Nucleoprotein TPR,TPR
Q7Z434,CARD adapter inducing interferon beta;Interferon beta promoter stimulator protein 1;Mitochondrial antiviral-signaling protein;Putative NF-kappa-B-activating protein 031N;Virus-induced-signaling adapter,IPS1;KIAA1271;MAVS;VISA
Q15291,Retinoblastoma-binding protein 5;Retinoblastoma-binding protein RBQ-3,RBBP5;RBQ3
Q5VWZ2,Lysophospholipase-like protein 1,LYPLAL1
Q9UPN9,E3 ubiquitin-protein ligase TRIM33;Ectodermin homolog;RET-fused gene 7 protein;Transcription intermediary factor 1-gamma;Tripartite motif-containing protein 33,KIAA1113;RFG7;TIF1G;TRIM33
Q32MZ4,GC-binding factor 2;Leucine-rich repeat flightless-interacting protein 1;TAR RNA-interacting protein,GCF2;LRRFIP1;TRIP
O00410,"Importin subunit beta-3;Importin-5;Karyopherin beta-3;Ran-binding protein 5;cDNA FLJ54573, highly similar to Importin beta-3",IPO5;KPNB3;RANBP5
Q96EA4,Arsenite-related gene 1 protein;Coiled-coil domain-containing protein 99;Protein Spindly;Rhabdomyosarcoma antigen MU-RMS-40.4A;cDNA FLJ55024,CCDC99
Q5W0B1,RING finger protein 219,C13orf7;RNF219
Q9UHI6,Component of gems 3;DEAD box protein 20;DEAD box protein DP 103;Gemin-3;Probable ATP-dependent RNA helicase DDX20,DDX20;DP103;GEMIN3
Q9NWZ8,Gem-associated protein 8;Protein FAM51A1,FAM51A1;GEMIN8
P21266,Glutathione S-transferase Mu 3;GST class-mu 3;GSTM3-3,GST5;GSTM3
Q16822,"Phosphoenolpyruvate carboxykinase [GTP], mitochondrial;Phosphoenolpyruvate carboxylase;cDNA FLJ50710, highly similar to Phosphoenolpyruvate carboxykinase (GTP), mitochondrial (EC 4.1.1.32);cDNA, FLJ79105, highly similar to Phosphoenolpyruvate carboxykinase (GTP), mitochondrial (EC 4.1.1.32)",PCK2;PEPCK2
O43143,ATP-dependent RNA helicase #46;DEAH box protein 15;Putative pre-mRNA-splicing factor ATP-dependent RNA helicase DHX15,DBP1;DDX15;DHX15
Q13123,Cytokine IK;IK factor;Protein Red;Protein RER;Clone TCCCIA00142 mRNA sequence,IK;RED;RER
Q8ND24,RING finger protein 214;cDNA FLJ58281,RNF214